National Hemophilia Center, Institute of Thrombosis and Hemostasis, Sheba Medical Center, Tel-Hashomer, Israel; School of Medicine, Tel Aviv University, Israel; Department of Medicine and Surgery, University of Insubria, Varese, Italy.
Department of Medicine and Surgery, University of Insubria, Varese, Italy.
Thromb Res. 2024 Feb;234:75-85. doi: 10.1016/j.thromres.2023.12.014. Epub 2024 Jan 2.
Splanchnic vein thrombosis (SVT), a thrombosis which involves the portal, mesenteric, and splenic veins, and the Budd-Chiari syndrome, represents an uncommon type of venous thromboembolism (VTE). Like with deep vein thrombosis of the lower extremities and pulmonary embolism, ample evidence suggests a significant association between SVT and cancer, particularly intra-abdominal solid malignancies (e.g. hepatobiliary and pancreatic cancers) and myeloproliferative neoplasms (MPN). Clinical symptoms of SVT in cancer patients can be ambiguous, and frequently attributed to the primary cancer itself. Alternatively, SVT may be asymptomatic and detected incidentally during cancer staging or follow-up evaluations. SVT can also precede the diagnosis of cancer and has been associated with poorer outcomes in patients with liver or pancreatic cancers. Therefore, an unprovoked SVT warrants a thorough evaluation for an underlying malignancy or MPN. Cancer-associated SVT carries a high risk of VTE extension, recurrence and bleeding. Extended anticoagulant treatment is often required in the absence of a high bleeding risk. Guidelines suggest treatment with either low molecular weight heparin (LMWH) or direct oral anticoagulants (DOACs), although available data on the safety and effectiveness of DOACs in these patients is limited. This comprehensive review outlines the epidemiology, pathogenesis, risk factors, and diagnosis of cancer-associated SVT and underscores the importance of comprehensive patient evaluation and evidence-based management.
内脏静脉血栓形成(SVT)是一种涉及门静脉、肠系膜静脉和脾静脉的血栓形成,而 Budd-Chiari 综合征则代表了一种不常见的静脉血栓栓塞症(VTE)类型。与下肢深静脉血栓形成和肺栓塞一样,大量证据表明 SVT 与癌症之间存在显著关联,特别是腹腔内实体恶性肿瘤(如肝胆癌和胰腺癌)和骨髓增生性肿瘤(MPN)。癌症患者的 SVT 临床症状可能不明确,且常归因于原发性癌症本身。或者,SVT 可能无症状,在癌症分期或随访评估中偶然发现。SVT 也可能先于癌症诊断,并与肝癌或胰腺癌患者的预后较差相关。因此,对于无明显诱因的 SVT,需要彻底评估是否存在潜在恶性肿瘤或 MPN。与癌症相关的 SVT 有很高的 VTE 扩展、复发和出血风险。在没有高出血风险的情况下,通常需要进行抗凝治疗。指南建议使用低分子肝素(LMWH)或直接口服抗凝剂(DOACs)治疗,但在这些患者中 DOACs 的安全性和有效性的数据有限。本综述概述了与癌症相关的 SVT 的流行病学、发病机制、危险因素和诊断,并强调了全面评估患者和基于证据的管理的重要性。