Othman Feras, Anantha Sadhana, Ward Gavin H, Paulus Elizabeth, Romaguera Rita
General Surgery, University of Miami, Miami, USA.
School of Medicine, St. George's University School of Medicine, True Blue, GRD.
Cureus. 2023 Dec 11;15(12):e50314. doi: 10.7759/cureus.50314. eCollection 2023 Dec.
Intravascular papillary endothelial hyperplasia (IPEH), or Masson's tumor, is a rare and benign proliferation of endothelial cells typically of vascular origin. Common locations of Masson's tumor include the head, neck, orbit, lip, pharynx, and mandible. It is typically seen in middle-aged adult life and females. Possible differential diagnoses include hemangioma, benign vascular formation, angiosarcoma, and neurofibromatosis. The exact pathophysiology of Masson's tumor is currently unknown. We present the case of a middle-aged 47-year-old male with a pure type of Masson's tumor presenting with pedunculated, malleable lesions across the posterior scalp and circumferential neck, on the pinna of the right ear, and within the right external auditory meatus. The lesions within the right external auditory meatus caused conductive hearing loss. The plan is a complete surgical excision without wide margins. The patient was referred to an ear, nose, and throat (ENT) surgeon due to the complicated location of the lesion within the external auditory meatus. This case serves as a differential diagnosis of conductive hearing loss complicated by Masson's tumor.
血管内乳头状内皮增生（IPEH），即马松瘤，是一种罕见的良性内皮细胞增生，通常起源于血管。马松瘤的常见部位包括头部、颈部、眼眶、唇部、咽部和下颌骨。它多见于中年成年人，女性更为常见。可能的鉴别诊断包括血管瘤、良性血管形成、血管肉瘤和神经纤维瘤病。马松瘤的确切病理生理学目前尚不清楚。我们报告一例47岁中年男性的纯型马松瘤病例，其表现为后头皮、颈部周围、右耳廓及右外耳道内有带蒂、可塑形的病变。右外耳道内的病变导致传导性听力损失。治疗方案是完整手术切除，无需广泛切缘。由于病变位于外耳道内的位置复杂，患者被转诊至耳鼻喉科（ENT）外科医生处。该病例可作为马松瘤并发传导性听力损失的鉴别诊断。
