Sheptulin V A, Grusha Ya O
Krasnov Research Institute of Eye Diseases, Moscow, Russia.
I.M. Sechenov First Moscow State Medical University (Sechenov University), Moscow, Russia.
Vestn Oftalmol. 2023;139(6):144-150. doi: 10.17116/oftalma2023139061144.
Parry-Romberg syndrome (PRS) is a rare degenerative disease of unknown etiology, characterized by slow progressive hemifacial atrophy of the soft tissues (subcutaneous fat, muscles), cartilage and bones. Beside hemifacial atrophy, various ophthalmic and periocular manifestations of PRS has been described. Progressive enophthalmos and eyelid changes are only some of many other symptoms, as the disease can affect all layers of the eyeball. This article reviews literature on ophthalmic manifestations of PRS and reports our own case and treatment approach for a patient with this pathology.
帕里-罗姆伯格综合征（PRS）是一种病因不明的罕见退行性疾病，其特征为软组织（皮下脂肪、肌肉）、软骨和骨骼的缓慢进行性半侧面部萎缩。除了半侧面部萎缩外，PRS还存在各种眼部和眼周表现。进行性眼球内陷和眼睑改变只是众多其他症状中的一部分，因为该疾病可影响眼球的所有层次。本文回顾了关于PRS眼部表现的文献，并报告了我们对一名患有这种病症的患者的病例及治疗方法。
