Nephrology Service, Hospital Británico de Buenos Aires, Buenos Aires, Argentina.
Division of Nephrology and Hypertension, Mayo Clinic, Rochester, MN, USA.
J Nephrol. 2024 Apr;37(3):739-745. doi: 10.1007/s40620-023-01833-3. Epub 2024 Jan 18.
IgA nephropathy is the most common primary glomerulonephritis worldwide, and an important cause of kidney failure, as 20-40% of patients progress to renal replacement therapy 20-30 years after diagnosis. Its clinical presentation ranges from isolated microscopic hematuria to nephrotic syndrome, and even to a rapidly progressive course. Ethnicity and epigenetics play a key role in its clinical aggressiveness. Selection of patients at risk needing immunosuppressive treatment is a challenge for the nephrologist. Some active and chronic kidney lesions detected on kidney biopsy have been demonstrated to have prognostic value according to the Oxford Classification of IgA nephropathy, later validated by numerous studies. However, KDIGO 2021 guidelines still consider persistent proteinuria > 1 g/24 h to be the most relevant risk factor for the progression of IgA nephropathy and the only one requiring immunosuppressive treatment. KDIGO guidelines have proposed a therapeutic algorithm, but many patients present peculiar characteristics that are not addressed by the current guidelines, pointing to the need for alternative approaches. In these cases, a tailored approach to each patient should be followed in which clinical, histological, laboratory, social and ethical aspects must be considered. In this manuscript we present three cases of IgA nephropathy from different countries, highlighting many of the aspects encountered in clinical practice that illustrate an individualized approach to the treatment of these patients.
IgA 肾病是全球最常见的原发性肾小球肾炎,也是肾衰竭的一个重要病因,约 20-40%的患者在诊断后 20-30 年内进展为肾脏替代治疗。其临床表现范围从孤立性镜下血尿到肾病综合征,甚至是快速进展性病程。种族和表观遗传学在其临床侵袭性中起着关键作用。选择需要免疫抑制治疗的高危患者是肾病学家面临的挑战。一些在肾活检中检测到的活动性和慢性肾脏病变,根据 IgA 肾病的牛津分类,具有预后价值,后来被许多研究证实。然而,KDIGO 2021 指南仍然认为持续性蛋白尿 > 1g/24h 是 IgA 肾病进展的最相关危险因素,也是唯一需要免疫抑制治疗的危险因素。KDIGO 指南提出了一个治疗算法,但许多患者具有目前指南未涉及的特殊特征,这表明需要替代方法。在这些情况下,应该对每个患者采用量身定制的方法,必须考虑临床、组织学、实验室、社会和伦理方面。在本文中,我们介绍了来自不同国家的 3 例 IgA 肾病病例,突出了临床实践中遇到的许多方面,说明了对这些患者进行个体化治疗的必要性。