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右心房原发性心脏淋巴瘤导致心力衰竭。

Right Atrium Primary Cardiac Lymphoma Causing Heart Failure.

作者信息

Doño Angel, Lounsbury Cassidy, Garrett Harvey Edward

机构信息

Department of Surgery, The University of Tennessee Health Science Center, Memphis, Tennessee, United States.

The Cardiovascular Surgery Clinic, Memphis, Tennessee, United States.

出版信息

Thorac Cardiovasc Surg Rep. 2024 Jan 22;13(1):e1-e3. doi: 10.1055/a-2228-7405. eCollection 2024 Jan.

DOI:10.1055/a-2228-7405
PMID:38264199
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10803137/
Abstract

Patients with primary cardiac tumors may present with symptoms based on the size and location of the tumor. Symptoms may include congestive heart failure secondary to intracardiac obstruction, systemic embolization, arrhythmias, and constitutional symptoms.  A patient presented with new onset atrial fibrillation and heart failure. Workup including open surgery revealed a primary cardiac lymphoma.  Cardiac tumors present with a variety of symptoms and are best evaluated by echocardiogram, computed tomography angiography, and magnetic resonance imaging. Tissue diagnosis is necessary. Although primary cardiac lymphoma is rare, long-term survival after chemotherapy and rituximab is superior to other cardiac malignancies.

摘要

原发性心脏肿瘤患者可能会根据肿瘤的大小和位置出现症状。症状可能包括因心内梗阻继发的充血性心力衰竭、全身性栓塞、心律失常和全身症状。一名患者出现新发房颤和心力衰竭。包括开放手术在内的检查发现了原发性心脏淋巴瘤。心脏肿瘤会出现多种症状,最好通过超声心动图、计算机断层血管造影和磁共振成像进行评估。组织诊断是必要的。虽然原发性心脏淋巴瘤很少见,但化疗和利妥昔单抗治疗后的长期生存率优于其他心脏恶性肿瘤。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5476/10803137/658307cbad45/10-1055-a-2228-7405-i1120230483crc-3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5476/10803137/8e5ad3073c0c/10-1055-a-2228-7405-i1120230483crc-1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5476/10803137/b4eecafe1c1d/10-1055-a-2228-7405-i1120230483crc-2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5476/10803137/658307cbad45/10-1055-a-2228-7405-i1120230483crc-3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5476/10803137/8e5ad3073c0c/10-1055-a-2228-7405-i1120230483crc-1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5476/10803137/b4eecafe1c1d/10-1055-a-2228-7405-i1120230483crc-2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5476/10803137/658307cbad45/10-1055-a-2228-7405-i1120230483crc-3.jpg

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本文引用的文献

1
Cardiac myxomas: causes, presentations, diagnosis, and management.心脏黏液瘤:病因、临床表现、诊断和治疗。
Ir J Med Sci. 2024 Apr;193(2):677-688. doi: 10.1007/s11845-023-03531-2. Epub 2023 Sep 22.
2
Long-Term Outcomes of Primary Cardiac Lymphoma.原发性心脏淋巴瘤的长期预后
Circulation. 2020 Dec;142(22):2194-2195. doi: 10.1161/CIRCULATIONAHA.120.047215. Epub 2020 Nov 30.
3
Primary cardiac tumors.原发性心脏肿瘤
Tex Heart Inst J. 2011;38(3):261-2.
4
Right heart sarcomas.右心肉瘤
Methodist Debakey Cardiovasc J. 2010 Jul-Sep;6(3):44-8. doi: 10.14797/mdcj-6-3-44.
5
Malignant tumor overview.恶性肿瘤概述
Methodist Debakey Cardiovasc J. 2010 Jul-Sep;6(3):35-7. doi: 10.14797/mdcj-6-3-35.