Yuge Norihisa, Manabe Susumu, Hirayama Daiki, Yamada Ryuki, Hori Mariko, Saito Tomohiro, Mochizuki Nobuhiro, Sugimura Koichiro, Shimokawa Hiroaki
Department of Cardiac Surgery, International University of Health and Welfare Narita Hospital.
Department of Cardiology, International University of Health and Welfare Narita Hospital.
Int Heart J. 2024;65(1):155-158. doi: 10.1536/ihj.23-401.
Unroofed coronary sinus syndrome is a rare congenital cardiac anomaly, involving some anatomical variations. Approximately 60% of patients with unroofed coronary sinus syndrome have a concomitant atrial septal defect, which is termed unroofed coronary sinus atrial septal defect (CSASD). The precise detection of these abnormalities has been usually difficult with conventional echocardiography, mostly due to its small and complex structures. Herein, we report a case with unroofed coronary sinus atrial septal defect, in which preoperative contrast-enhanced computed tomography (CT) was useful in the operative decision making. We successfully repaired the defective roof of the coronary sinus with a bovine patch, while eliminating the inter-atrial shunt. The patient's postoperative course was uneventful with no residual shunt.
无顶冠状静脉窦综合征是一种罕见的先天性心脏异常，涉及一些解剖变异。约60%的无顶冠状静脉窦综合征患者伴有房间隔缺损，称为无顶冠状静脉窦型房间隔缺损（CSASD）。由于这些异常结构小且复杂，传统超声心动图通常难以精确检测。在此，我们报告一例无顶冠状静脉窦型房间隔缺损病例，术前对比增强计算机断层扫描（CT）对手术决策很有用。我们成功地用牛心包补片修复了冠状静脉窦的缺损顶，同时消除了心房分流。患者术后恢复顺利，无残余分流。
