Chaisrisawadisuk Sarut, Khampalikit Inthira, Chankaew Ekawut, Moore Mark H
Division of Plastic Surgery, Department of Surgery, Faculty of Medicine Siriraj Hospital, Mahidol University, Bangkok, Thailand.
Cleft and Craniofacial South Australia, Women's and Children's Hospital, North Adelaide, SA, Australia.
Childs Nerv Syst. 2024 Jun;40(6):1937-1941. doi: 10.1007/s00381-024-06309-8. Epub 2024 Feb 7.
Cloverleaf skull deformity or Kleeblattschadel syndrome is a severe condition where multiple cranial sutures are absent and prematurely fused, leading to a trilobate head shape. The remaining open sutures or fontanelles compensate for rapid brain expansion, while the constricted fused calvarium restricts brain growth and results in increased intracranial pressure. Recent data show that early posterior cranial and foramen magnum decompression positively affects infants with cloverleaf skulls. However, long-term sequelae are still rarely discussed. We hereby report a child who developed secondary metopic craniosynostosis after posterior cranial decompression, which required a front-orbital advancement and cranial remodelling as a definitive procedure.
三叶草颅骨畸形或 Kleeblattschadel 综合征是一种严重的病症，表现为多条颅缝缺失且过早融合，导致头部呈三叶形。剩余开放的颅缝或囟门可补偿大脑的快速扩张，而狭窄融合的颅骨则限制大脑生长并导致颅内压升高。近期数据表明，早期进行后颅窝和枕骨大孔减压对患有三叶草颅骨畸形的婴儿有积极影响。然而，长期后遗症仍很少被讨论。我们在此报告一名儿童，其在进行后颅窝减压后出现了继发性额缝早闭，这需要进行额眶前移和颅骨重塑作为确定性手术。
