Posar Annio, Visconti Paola
IRCCS Istituto delle Scienze Neurologiche di Bologna, UOSI Disturbi dello Spettro Autistico, 40139 Bologna, Italy.
Department of Biomedical and Neuromotor Sciences, Bologna University, 40139 Bologna, Italy.
Children (Basel). 2024 Jan 28;11(2):169. doi: 10.3390/children11020169.
In the context of childhood epilepsy, the concept of continuous spike-waves during slow sleep (CSWS) includes several childhood-onset heterogeneous conditions that share electroencephalograms (EEGs) characterized by a high frequency of paroxysmal abnormalities during sleep, which have negative effects on the cognitive development and behavior of the child. These negative effects may have the characteristics of a clear regression or of a slowdown in development. Seizures are very often present, but not constantly. The above makes it clear why CSWS have been included in epileptic encephalopathies, in which, by definition, frequent EEG paroxysmal abnormalities have an unfavorable impact on cognitive functions, including socio-communicative skills, causing autistic features, even regardless of the presence of clinically overt seizures. Although several decades have passed since the original descriptions of the electroclinical condition of CSWS, there are still many areas that are little-known and deserve to be further studied, including the EEG diagnostic criteria, the most effective electrophysiological parameter for monitoring the role of the thalamus in CSWS pathogenesis, its long-term evolution, the nosographic location of Landau-Kleffner syndrome, standardized neuropsychological and behavioral assessments, and pharmacological and non-pharmacological therapies.
在儿童癫痫的背景下,慢波睡眠期持续棘慢波(CSWS)的概念包括几种儿童期起病的异质性疾病,这些疾病的脑电图(EEG)特征为睡眠期间阵发性异常频率较高,对儿童的认知发展和行为产生负面影响。这些负面影响可能具有明显倒退或发育迟缓的特征。癫痫发作经常出现,但并非持续存在。上述情况清楚地说明了为什么CSWS被纳入癫痫性脑病,根据定义,频繁的EEG阵发性异常对认知功能,包括社会交往技能,产生不利影响,导致自闭症特征,即使在没有临床明显癫痫发作的情况下也是如此。尽管自最初描述CSWS的电临床状况以来已经过去了几十年,但仍有许多领域鲜为人知,值得进一步研究,包括EEG诊断标准、监测丘脑在CSWS发病机制中作用的最有效电生理参数、其长期演变、Landau-Kleffner综合征的疾病分类定位、标准化神经心理学和行为评估以及药物和非药物治疗。