Rizk Ryan C, Yasrab Mohammad, Chu Linda C, Weisberg Edmund M, Fishman Elliot K
The Russell H. Morgan Department of Radiology and Radiological Science, Johns Hopkins University School of Medicine, 601 North Caroline St, Baltimore, MD 21287 USA.
Radiol Case Rep. 2024 Feb 21;19(5):1815-1818. doi: 10.1016/j.radcr.2024.01.080. eCollection 2024 May.
Sclerosing epithelioid fibrosarcoma is a rare fibrosarcoma variant in which more than half of patients experience local recurrence or metastatic spread. In the current literature, there is limited and nonspecific imaging data, contributing to frequent misdiagnosis and delays in treatment intervention. Given the poor prognosis associated with this malignancy and the high probability of metastases, accurate and prompt diagnoses are critical. In this article, we report the case of a 27-year-old female diagnosed with metastatic sclerosing epithelioid fibrosarcoma following the discovery of a growing palpable mass on her right gluteus maximus muscle. We focus on the use of radiological imaging modalities in optimizing diagnosis and correlate our imaging and pathological findings.
硬化性上皮样纤维肉瘤是一种罕见的纤维肉瘤变体，超过半数患者会出现局部复发或转移扩散。在当前文献中，影像学数据有限且缺乏特异性，导致频繁误诊和治疗干预延迟。鉴于这种恶性肿瘤的预后较差且转移可能性高，准确及时的诊断至关重要。在本文中，我们报告了一例27岁女性病例，该患者在右臀大肌发现一个可触及的不断增大的肿块后，被诊断为转移性硬化性上皮样纤维肉瘤。我们重点关注放射影像学检查方法在优化诊断中的应用，并将我们的影像学和病理学发现进行关联。
