Kumar Rohini, Blackband Jamie, Wagle Shukla Aparna
Department of Neurology, Norman Fixel Institute for Neurological Diseases, University of Florida, Gainesville, Florida, United States of America.
Tremor Other Hyperkinet Mov (N Y). 2024 Feb 29;14:8. doi: 10.5334/tohm.845. eCollection 2024.
Jaw clonus refers to involuntary, rhythmic jaw contractions induced by a hyperactive trigeminal nerve stretch reflex; however, the movements, when triggered without a stretch, can be confused with a tremor.
This video demonstrates a patient with amyotrophic lateral sclerosis presenting with rapid rhythmic jaw movements seen at rest, alongside a power spectrum analysis revealing a narrow high-frequency peak of 10 Hz.
Rhythmic jaw movements are seen in many disorders such as Parkinson's disease, essential tremor, tardive syndromes, and cranial myorhythmias; however, a high-frequency movement, regardless of clonus or tremor, can indicate amyotrophic lateral sclerosis when accompanied by typical upper and lower motor neuron signs.
The presented video abstract shows a patient with amyotrophic lateral sclerosis with rhythmic jaw movements seen at rest. A power spectrum analysis of the rhythmic movements revealed a 10 Hz peak, a frequency higher than those seen in patients with Parkinson's disease, essential tremor, myorhythmia, and tardive syndromes.
下颌阵挛是指由三叉神经牵张反射亢进引起的不自主、有节律的下颌收缩；然而，在无牵张刺激时触发的运动可能会与震颤相混淆。
本视频展示了一名肌萎缩侧索硬化患者，其在静息状态下出现快速有节律的下颌运动，同时功率谱分析显示有一个10赫兹的狭窄高频峰值。
有节律的下颌运动可见于许多疾病，如帕金森病、特发性震颤、迟发性综合征和颅肌节律障碍；然而，高频运动，无论为阵挛还是震颤，当伴有典型的上下运动神经元体征时，可能提示肌萎缩侧索硬化。
所展示的视频摘要显示一名肌萎缩侧索硬化患者在静息状态下有节律的下颌运动。对这些有节律运动的功率谱分析显示有一个10赫兹的峰值，该频率高于帕金森病、特发性震颤、肌节律障碍和迟发性综合征患者所观察到的频率。
