Sahni Manish, Singh Suresh, Lakhera Kamal Kishore, Babu Agil, Sharma Rajgovind
Department of Surgical Oncology, SMS Medical College and Hospital, Jaipur, Rajasthan India.
M.G Medical College, Jaipur, Rajasthan India.
Indian J Otolaryngol Head Neck Surg. 2024 Feb;76(1):1430-1433. doi: 10.1007/s12070-023-04225-y. Epub 2023 Sep 16.
Fibromatosis is a rare locally aggressive benign tumour which arises from the musculoaponeurotic structures throughout the body. In the oral and maxillofacial region, It has been described under a variety of synonyms, including 'extra articular desmoids', 'desmoids tumours', 'grade-1 fibrosarcomas','non metastasizing fibrosarcoma'and 'aggressive fibromatosis'. The pecularity of this entity in paranasal sinuses is that it is rare in this location and are locally aggressive with higher rates of recurrence in a relatively restricted area.The purpose of this study is to present a rare case report and reviewing the literature of this entity.
纤维瘤病是一种罕见的局部侵袭性良性肿瘤,起源于全身的肌筋膜结构。在口腔颌面部区域,它有多种同义词,包括“关节外硬纤维瘤”“硬纤维瘤”“1级纤维肉瘤”“非转移性纤维肉瘤”和“侵袭性纤维瘤病”。该病变在鼻窦的特殊性在于它在这个部位很罕见,并且在相对局限的区域具有局部侵袭性和较高的复发率。本研究的目的是报告1例罕见病例并复习该病变的相关文献。