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孤立性心脏结节病伴严重左心室收缩功能障碍自发缓解,无需类固醇治疗。

Spontaneous Remission Without Steroid Therapy in Isolated Cardiac Sarcoidosis with Severe Left Ventricular Systolic Dysfunction.

机构信息

Department of Cardiology, Fukuyama Cardiovascular Hospital.

Department of Cardiovascular Medicine, Hiroshima University Hospital.

出版信息

Int Heart J. 2024 Mar 30;65(2):359-362. doi: 10.1536/ihj.23-399. Epub 2024 Mar 12.

Abstract

Spontaneous remission is often observed in extracardiac cases of sarcoidosis, such as skin sarcoidosis. However, for cardiac sarcoidosis (CS), the prognosis is unfavorable. Although corticosteroids are the first-line treatment for CS, data regarding the natural history of isolated CS are limited. We describe a rare case of isolated CS with severe left ventricular systolic dysfunction that improved without steroid therapy.

摘要

在皮肤结节病等心脏外结节病病例中,常可观察到自发缓解。然而,对于心脏结节病(CS),预后不佳。虽然皮质类固醇是 CS 的一线治疗药物,但关于孤立性 CS 的自然病史的数据有限。我们描述了一例罕见的孤立性 CS 伴有严重左心室收缩功能障碍的病例,该病例在未接受类固醇治疗的情况下得到改善。

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