Department of Medical Education, National Taiwan University Hospital, Taipei, Taiwan.
Department of Dermatology, National Taiwan University Hospital, Taipei, Taiwan.
Exp Dermatol. 2024 Mar;33(3):e15056. doi: 10.1111/exd.15056.
Several studies have suggested that mutation of the interleukin 36 receptor antagonist gene (IL36RN) is related to generalized pustular psoriasis (GPP), and the presence of IL36RN mutation may affect the clinical manifestations and treatment responses. However, genetic testing is not routinely available in clinical practice for the diagnosis of GPP. Previously, GPP patients with acrodermatitis continua of Hallopeau (ACH) were found to have a high percentage of carrying IL36RN mutation. In this study, we reported six patients with pustular psoriasis presenting as diffuse palmoplantar erythema with keratoderma among 60 patients who carried IL36RN mutation. ACH was present in five patients and five patients had acute flare of GPP. This unique presentation may serve as a predictor for IL36RN mutation in patients with pustular psoriasis, similar to ACH.
几项研究表明,白细胞介素 36 受体拮抗剂基因(IL36RN)突变与泛发性脓疱型银屑病(GPP)有关,IL36RN 突变的存在可能影响临床表现和治疗反应。然而,遗传检测在临床实践中并不常规用于 GPP 的诊断。先前发现,具有 Hallopeau 连续性肢端皮炎(ACH)的 GPP 患者携带 IL36RN 突变的比例很高。在这项研究中,我们报告了 60 例携带 IL36RN 突变的患者中,有 6 例脓疱性银屑病患者表现为弥漫性手掌和足底红斑伴角化过度。5 例患者存在 ACH,5 例患者 GPP 急性发作。这种独特的表现可能是脓疱性银屑病患者 IL36RN 突变的预测因子,类似于 ACH。