皮下脂膜炎样 T 细胞淋巴瘤：以发热和面部肿胀为表现的噬血细胞综合征
Subcutaneous panniculitis-like T-cell lymphoma: fever and facial swelling with hemophagocytic syndrome.
机构信息
Department of Medicine, All India Institute of Medical Sciences, New Delhi, Delhi, India.
Department of Pathology, All India Institute of Medical Sciences, New Delhi, Delhi, India.
出版信息
BMJ Case Rep. 2024 Apr 2;17(4):e256615. doi: 10.1136/bcr-2023-256615.
Abstract
We report a case of subcutaneous panniculitis-like T-cell lymphoma (SPTCL) in a young man presenting with fever and facial swelling. He had pancytopenia and hemophagocytic syndrome (HPS) on evaluation. The histopathological examination of skin punch biopsy from the face and chest wall showed SPTCL. Given the associated HPS, he was started on steroid and multidrug chemotherapy following which he had symptomatic improvement.
摘要
我们报告了一例发生于年轻男性的皮下脂膜炎样 T 细胞淋巴瘤（SPTCL），该患者以发热和面部肿胀为表现。评估时患者存在全血细胞减少和噬血细胞综合征（HPS）。来自面部和胸壁的皮肤打孔活检的组织病理学检查显示为 SPTCL。鉴于存在相关的 HPS，给予他类固醇和多药化疗，随后他的症状得到改善。
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