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一名17岁原发性血小板增多症患者获得性血管性血友病综合征:病例报告及文献复习

Acquired von Willebrand Syndrome in a 17-Year-Old With Essential Thrombocythemia: A Case Report With Literature Review.

作者信息

Youn Linda, Kuta Amber, Srinivasan Mirra, Mahatara Renuka, Khalil Mazen

机构信息

Internal Medicine, St. Bernards Medical Center, Jonesboro, USA.

Internal Medicine, New York Institute of Technology College of Osteopathic Medicine, Jonesboro, USA.

出版信息

Cureus. 2024 Mar 6;16(3):e55668. doi: 10.7759/cureus.55668. eCollection 2024 Mar.

DOI:10.7759/cureus.55668
PMID:38586809
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10995757/
Abstract

Acquired von Willebrand syndrome (AVWS) is a rare bleeding disorder that is often underdiagnosed. AVWS typically occurs in adults without a family history of bleeding disorders and with associated conditions such as lymphoproliferative, myeloproliferative, and cardiovascular disorders. Here, we present a case of AVWS in a young patient with essential thrombocythemia and a literature review on AVWS in the setting of essential thrombocythemia.

摘要

获得性血管性血友病综合征(AVWS)是一种罕见的出血性疾病,常常未被诊断出来。AVWS通常发生在没有出血性疾病家族史且伴有如淋巴增殖性、骨髓增殖性和心血管疾病等相关病症的成年人中。在此,我们报告一例患有原发性血小板增多症的年轻患者的AVWS病例,并对原发性血小板增多症背景下的AVWS进行文献综述。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c9dc/10995757/40969271bdc1/cureus-0016-00000055668-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c9dc/10995757/40969271bdc1/cureus-0016-00000055668-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c9dc/10995757/40969271bdc1/cureus-0016-00000055668-i01.jpg

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本文引用的文献

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J Lab Physicians. 2021 Sep;13(3):195-201. doi: 10.1055/s-0041-1730818. Epub 2021 Jun 28.
2
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Transfusion. 2021 Nov;61(11):3277-3280. doi: 10.1111/trf.16682. Epub 2021 Sep 26.
3
Triple-Negative Essential Thrombocythemia Complicated by Thrombosis and Acquired von Willebrand Disease in a Young Man.
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Am J Case Rep. 2020 Aug 23;21:e924560. doi: 10.12659/AJCR.924560.
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Case Rep Oncol. 2020 Jun 26;13(2):733-737. doi: 10.1159/000507883. eCollection 2020 May-Aug.
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Essential Thrombocythemia and Acquired von Willebrand Syndrome: The Shadowlands between Thrombosis and Bleeding.原发性血小板增多症与获得性血管性血友病综合征:血栓形成与出血之间的模糊地带
Cancers (Basel). 2020 Jun 30;12(7):1746. doi: 10.3390/cancers12071746.
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Acquired von Willebrand syndrome: focused for hematologists.获得性血管性血友病:血液科重点关注。
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