Okorozo Aham, Chiang Vicky, Kim Hyun S, Vimolratana Marc, Sadoughi Ali
Pulmonary Division-Department of Medicine, Montefiore Medical Center-Albert Einstein College of Medicine, Bronx, NY, USA.
Department of Surgery, Thoracic Surgery, Montefiore Medical Center-Albert Einstein College of Medicine, Bronx, N.Y, USA.
Respir Med Case Rep. 2024 May 1;50:102024. doi: 10.1016/j.rmcr.2024.102024. eCollection 2024.
Straight-back syndrome is a rare congenital condition involving the loss of the normal dorsal curvature of the upper thoracic spine. This leads to flattening of the upper thoracic cavity, resulting in compression of the underlying vasculature and airways. In this case report, we discuss the management of an 18-year-old male with straight-back syndrome who was referred to our interventional pulmonary clinic for further management of his stridor and apneic events. A trial of airway stenting was done which resolved the patient's respiratory symptoms. Definitive surgical correction was not applicable due to other significant medical conditions, but tracheostomy provided a sustainable alternative treatment. Tracheostomy tube placement and airway stenting are reasonable alternatives to surgery for patients who experience airway obstruction due to straight-back syndrome. Stent placement may also relieve respiratory symptoms but is associated with a higher rate of complications.
直背综合征是一种罕见的先天性疾病,涉及上胸椎正常后凸消失。这会导致上胸腔变平,从而压迫其下方的血管和气道。在本病例报告中,我们讨论了一名18岁直背综合征男性患者的治疗情况,该患者被转诊至我们的介入肺科门诊,以进一步处理其喘鸣和呼吸暂停事件。进行了气道支架置入试验,该试验缓解了患者的呼吸症状。由于其他严重的医疗状况,无法进行确定性手术矫正,但气管造口术提供了一种可持续的替代治疗方法。对于因直背综合征导致气道阻塞的患者,气管造口管置入和气道支架置入是手术的合理替代方案。支架置入也可能缓解呼吸症状,但并发症发生率较高。