Zebbakh Hajar, Imrani Kaoutar, Aaboudech Taha Yassine, Bernoussi Zakia, MoatassimBillah Nabil, Nassar Ittimade
Central radiology department, Ibn Sina University Hospital, Rabat, Maroc.
Central department of pathological anatomy and cytology, Ibn Sina University Hospital, Rabat, Maroc.
Radiol Case Rep. 2024 May 4;19(8):3023-3027. doi: 10.1016/j.radcr.2024.03.079. eCollection 2024 Aug.
Pheochromocytoma, a neuroendocrine tumor, represents a rare medical condition characterized by the excessive secretion of catecholamines. These tumors often exhibit distinctive features on imaging studies, notably appearing hypervascular. Furthermore, they may present as cystic masses with thin walls, a characteristic that becomes more evident following the administration of contrast medium. The cystic form of adrenal pheochromocytoma, as exemplified in our case, is particularly uncommon, thus underscoring the importance of recognizing its atypical presentation. Accurate diagnosis hinges on a thorough understanding of both the clinical manifestations and radiological findings suggestive of pheochromocytoma. However, definitive confirmation typically necessitates histological examination of the surgical specimen post-adrenalectomy. By shedding light on this rare variant, our case emphasizes the critical role of comprehensive diagnostic approaches in managing such complex medical conditions. Additionally, it underscores the significance of multidisciplinary collaboration among clinicians, radiologists, and pathologists to ensure timely and accurate diagnosis, ultimately guiding appropriate treatment strategies and optimizing patient outcomes.
嗜铬细胞瘤是一种神经内分泌肿瘤,是一种罕见的病症,其特征是儿茶酚胺分泌过多。这些肿瘤在影像学检查中常表现出独特的特征,尤其是表现为血管丰富。此外,它们可能表现为薄壁囊性肿块,在注射造影剂后这一特征会更加明显。如我们病例所示的肾上腺嗜铬细胞瘤囊性形式尤为罕见,因此凸显了认识其非典型表现的重要性。准确诊断取决于对提示嗜铬细胞瘤的临床表现和影像学发现的全面理解。然而,明确确诊通常需要在肾上腺切除术后对手术标本进行组织学检查。通过揭示这种罕见变体,我们的病例强调了综合诊断方法在管理此类复杂病症中的关键作用。此外,它还强调了临床医生、放射科医生和病理学家之间多学科协作的重要性,以确保及时准确的诊断,最终指导适当的治疗策略并优化患者预后。