Department of Nephrology, Fuyang People's Hospital, Anhui Medical University, Fuyang, Anhui, China.
Department of Nephrology, Shenzhen Hospital, Southern Medical University, Shenzhen, China.
Stem Cell Res. 2024 Jun;77:103439. doi: 10.1016/j.scr.2024.103439. Epub 2024 May 9.
Hypophosphatemic vitamin D-resistant rickets typically presents in infancy or early childhood with skeletal deformities and growth plate abnormalities. In this report, the SMUSHi005-A human induced pluripotent stem cell (hiPSC) line was successfully established from the PBMCs of a female patient carrying the PHEX mutation with c.1586-1586+1 delAG. The iPSC line has been confirmed to have a normal karyotype. The displayed cells clearly exhibit characteristics similar to embryonic stem cells, expressing pluripotency markers and demonstrating the ability to differentiate into three germ layers.
低磷抗维生素 D 性佝偻病通常在婴儿期或幼儿期出现,表现为骨骼畸形和生长板异常。本研究报告中,我们成功地从一位携带 PHEX 基因突变 c.1586-1586+1delAG 的女性患者的 PBMCs 中建立了 SMUSHi005-A 人诱导多能干细胞(hiPSC)系。该 iPSC 系已被证实具有正常核型。所展示的细胞明显表现出与胚胎干细胞相似的特征,表达多能性标记物,并具有分化为三个胚层的能力。