Translational Immunology Unit, Institut Pasteur, Université Paris-Cité, Paris, France; Department of Internal Medicine, Hôpital Bichat, Paris, France; Université Paris-Cité, Centre de Recherche sur l'Inflammation, INSERM UMR1149, CNRS ERL8252, Faculté de Médecine site Bichat, Laboratoire d'Excellence Inflamex, Paris, France.
Translational Immunology Unit, Institut Pasteur, Université Paris-Cité, Paris, France; Department of Internal Medicine, Hôpital Bichat, Paris, France.
Trends Immunol. 2024 Jun;45(6):406-418. doi: 10.1016/j.it.2024.04.013. Epub 2024 May 24.
Sarcoidosis is a chronic immune disease of unknown origin for which we still lack an immunological framework unifying causal agents, host factors, and natural history of disease. Here, we discuss the initial triggers of disease, and how myeloid cells drive granuloma formation and contribute to immunopathogenesis. We highlight recent advances in our understanding of innate immune memory and propose the hypothesis that maladaptive innate immune training connects previous environmental exposure to granuloma maintenance and expansion. Lastly, we consider how this hypothesis may open novel therapeutic avenues, while corticosteroids remain the front-line treatment.
结节病是一种病因不明的慢性免疫性疾病,我们仍然缺乏一个统一的病因、宿主因素和疾病自然史的免疫学框架。在这里,我们讨论疾病的初始触发因素,以及髓样细胞如何驱动肉芽肿形成并促进免疫发病机制。我们强调了我们对先天免疫记忆的理解的最新进展,并提出了一个假设,即适应性先天免疫训练将以前的环境暴露与肉芽肿的维持和扩张联系起来。最后,我们考虑了这一假设如何开辟新的治疗途径,而皮质类固醇仍然是一线治疗方法。