Princess Máxima Center for Pediatric Oncology, Utrecht.
Princess Máxima Center for Pediatric Oncology, Utrecht; Pediatric Oncology, Erasmus MC-Sophia Children's Hospital, Rotterdam, the Netherlands.
Haematologica. 2024 Jun 1;109(6):1700-1712. doi: 10.3324/haematol.2023.283815.
The treatment of childhood acute lymphoblastic leukemia (ALL) has reached overall survival rates exceeding 90%. The present and future challenges are to cure the remainder of patients still dying from disease, and to reduce morbidity and mortality in those who can be cured with standard-of-care chemotherapy by replacing toxic chemotherapy elements while retaining cure rates. With the novel therapeutic options introduced in the last years, including immunotherapies and targeted antibodies, the treatment of ALL is undergoing major changes. For B-cell precursor ALL, blinatumomab, an anti-CD19 bispecific antibody, has established its role in the consolidation treatment for both high- and standard-risk first relapse of ALL, in the presence of bone marrow involvement, and may also have an impact on the outcome of high-risk subsets such as infant ALL and Philadelphia chromosome-positive ALL. Inotuzumab ozogamicin, an anti-CD22 drug conjugated antibody, has demonstrated high efficacy in inducing complete remission in relapsed ALL, even in the presence of high tumor burden, but randomized phase III trials are still ongoing. For T-ALL the role of CD38-directed treatment, such as daratumumab, is gaining interest, but randomized data are needed to assess its specific benefit. These antibodies are currently being tested in patients with newly diagnosed ALL and may lead to major changes in the present paradigm of treatment of pediatric ALL. Unlike the past, lessons may be learned from innovations in adult ALL, in which more drastic changes are piloted that may need to be translated to pediatrics.
儿童急性淋巴细胞白血病 (ALL) 的治疗已达到总生存率超过 90%。目前和未来的挑战是治愈其余仍死于疾病的患者,并通过用毒性化疗药物替代标准治疗化疗中的有毒元素,同时保留治愈率,从而降低那些可以通过标准治疗治愈的患者的发病率和死亡率。随着近年来引入的新型治疗选择,包括免疫疗法和靶向抗体,ALL 的治疗正在发生重大变化。对于 B 细胞前体 ALL,blinatumomab(一种抗 CD19 双特异性抗体)已在存在骨髓受累的情况下确立了其在 ALL 首次高风险和标准风险复发巩固治疗中的作用,并且可能对高危亚组(如婴儿 ALL 和费城染色体阳性 ALL)的结局产生影响。Inotuzumab ozogamicin(一种抗 CD22 药物偶联抗体)已证明在复发 ALL 中诱导完全缓解的高疗效,即使存在高肿瘤负荷,但仍在进行随机 III 期试验。对于 T-ALL,CD38 靶向治疗(如 daratumumab)的作用引起了关注,但仍需要随机数据来评估其特定益处。这些抗体目前正在新诊断为 ALL 的患者中进行测试,可能会导致儿科 ALL 治疗目前模式的重大变化。与过去不同,成人 ALL 中的创新可能会吸取教训,在成人 ALL 中,进行了更激进的变革,这些变革可能需要转化为儿科。