Zebbakh Hajar, Sidki Kenza, Laamrani Fatima Zahra, Jroundi Laila, Aoufir Omar El
Emergency radiology department, Ibn Sina University Hospital, Rabat, Maroc.
Radiol Case Rep. 2024 May 21;19(8):3321-3323. doi: 10.1016/j.radcr.2024.04.075. eCollection 2024 Aug.
Superior semicircular canal (SSC) dehiscence syndrome, also known as Minor syndrome, is a rare condition characterized by vestibular and cochlear symptoms linked to a defect in the bony roof of the SSC. The prevalence is estimated at 0.5%, with a male predominance. Dehiscence may result from abnormal bone development, becoming symptomatic due to minimal trauma or pressure changes. Clinical presentation varies based on dehiscence size and location, with dizziness and oscillatory movements triggered by pressure changes or loud sounds being common symptoms. Other manifestations include conductive hearing loss due to the formation of a ``third window'' in the inner ear. Diagnosis typically involves computed tomography, distinguishing SSCDS from otosclerosis. Surgical treatment is reserved for cases of disabling vestibular pathology, often involving sealing the dehiscence through various approaches.
上半规管（SSC）裂综合征，也称为米诺尔综合征，是一种罕见病症，其特征为与上半规管骨顶缺陷相关的前庭和耳蜗症状。据估计，患病率为0.5%，男性居多。裂可能由骨骼发育异常引起，因轻微创伤或压力变化而出现症状。临床表现因裂的大小和位置而异，压力变化或大声响引发的头晕和摆动性运动是常见症状。其他表现包括内耳形成“第三窗”导致的传导性听力损失。诊断通常涉及计算机断层扫描，以将上半规管裂综合征与耳硬化症区分开来。手术治疗适用于致残性前庭病变的病例，通常采用各种方法封闭裂。
