Ebstein 畸形的临床表现与治疗。
Clinical Presentation and Therapy of Ebstein Anomaly.
机构信息
Department of Pediatric Cardiology and Intensive Care, Ludwig Maximilians University, Munich, Germany.
Division of Pediatric Cardiology, Department of Pediatrics, Mayo Clinic College of Medicine, Rochester, MN, USA.
出版信息
Adv Exp Med Biol. 2024;1441:903-907. doi: 10.1007/978-3-031-44087-8_56.
Ebstein anomaly is a rare congenital heart defect, accounting for less than 1% of cardiac malformations and occurring in approximately 1 out of 210,000 live births. It is characterized by an abnormality of the tricuspid valve, where the valve is positioned lower than normal in the right ventricle. Although primarily a tricuspid valve defect, the right ventricle itself is often structurally abnormal and weakened (myopathic).
Ebstein 畸形是一种罕见的先天性心脏缺陷，占心脏畸形的比例不到 1%，每 210000 例活产儿中约有 1 例。其特征为三尖瓣异常，三尖瓣位置低于右心室正常位置。尽管主要是三尖瓣瓣叶的病变，但右心室本身通常也存在结构异常和弱化（心肌病变）。
Zotero 插件