Institute for Cardiomyopathies Heidelberg (ICH), University Hospital Heidelberg, Heidelberg, Germany.
, QC, Canada.
Adv Exp Med Biol. 2024;1441:909-914. doi: 10.1007/978-3-031-44087-8_57.
Ebstein anomaly (EA) is a rare, congenital cardiac defect of the tricuspid valve with a birth prevalence between 0.5 and 1 in 20,000 [1]. It is characterized by displacement of the tricuspid valve toward the apex of the right ventricle (RV) and "atrialization" of the RV (Fig. 57.1) [2]. EA accounts for about 0.5% of all congenital heart diseases (CHD) [2]. Depending on severity of the defect and due to heterogeneity of the disease, patient's presentation varies from severe heart failure symptoms and arrhythmia in neonatal life to asymptomatic adults.
Ebstein 畸形（EA）是一种罕见的三尖瓣先天性心脏缺陷，其发病率为每 20000 例中有 0.5 至 1 例[1]。其特征是三尖瓣向右心室（RV）的顶点移位和 RV 的“房化”（图 57.1）[2]。EA 约占所有先天性心脏病（CHD）的 0.5％[2]。根据缺陷的严重程度以及疾病的异质性，患者的表现从新生儿期的严重心力衰竭症状和心律失常到无症状的成年人各不相同。
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