起源于鼻腔的多形性透明变性血管扩张性肿瘤：一份CARE病例报告。
Pleomorphic hyalinizing angiectatic tumor originating in the nasal cavity: A CARE case report.
作者信息
Sun S, Que D, Pan B, Hu K
机构信息
Department of Radiation Oncology, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences & Peking Union Medical College, No. 1 Shuaifuyuan Wangfujing, Dongcheng District, Beijing 100730, People's Republic of China.
Department of Oncology, The Third Affiliated Hospital of Chongqing Medical University, Chongqing 401120, People's Republic of China.
出版信息
Eur Ann Otorhinolaryngol Head Neck Dis. 2025 Jan;142(1):38-41. doi: 10.1016/j.anorl.2024.05.003. Epub 2024 Jun 17.
INTRODUCTION
Pleomorphic hyalinizing angiectatic tumor (PHAT) is a rare low-grade malignant mesenchymal neoplasm. It commonly occurs in the limbs and trunk, with limited occurrences in the head and neck region. Only five cases of PHAT occurring in the head and neck have been reported in the literature to date. The etiology of PHAT remains unclear. We described a case of nasal cavity PHAT following CARE guidelines.
CASE SUMMARY
A 32-year-old male with PHAT originating in the nasal cavity recurred after two surgeries. Adjuvant radiotherapy was performed after the third surgery. The patient has been regularly followed up for 36months, and no tumor recurrence or metastasis has been observed.
DISCUSSION
PHAT is a rare soft tissue tumor known for its local aggressiveness. Because of a high risk of recurrence, extensive resection should be implemented, possibly completed by radiotherapy if resection cannot be complete because of proximity to at-risk structures.
引言
多形性透明变性血管扩张性肿瘤（PHAT）是一种罕见的低度恶性间叶性肿瘤。它通常发生于四肢和躯干，在头颈部区域较少见。迄今为止，文献中仅报道了5例发生于头颈部的PHAT。PHAT的病因尚不清楚。我们按照CARE指南描述了1例鼻腔PHAT病例。
病例摘要
1例起源于鼻腔的PHAT男性患者，在两次手术后复发。第三次手术后进行了辅助放疗。该患者已定期随访36个月，未观察到肿瘤复发或转移。
讨论
PHAT是一种罕见的软组织肿瘤，以局部侵袭性著称。由于复发风险高，应进行广泛切除，如果因靠近危险结构而无法完全切除，可能需联合放疗完成手术。
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