Richter B J, McNutt N S
Arch Dermatol. 1979 Nov;115(11):1325-8.
A patient has an acquired, scarring, bullous eruption. The severity of the cutaneous, ocular, esophageal, and laryngeal scarring was suggestive of cicatricial pemphigoid or the severely dystrophic forms of epidermolysis bullosa. Clinical features and histologic and immunofluorescence and electron microscopic study led to the diagnosis of epidermolysis bullosa acquisita. The spectrum of epidermolysis bullosa acquisita includes cases that closely approximate the severity of disease previously recognized only for the recessive form of epidermolysis bullosa dystrophica.
一名患者出现后天性瘢痕性大疱性皮疹。皮肤、眼部、食管和喉部瘢痕形成的严重程度提示瘢痕性类天疱疮或严重营养不良型大疱性表皮松解症。临床特征、组织学、免疫荧光及电子显微镜研究结果确诊为获得性大疱性表皮松解症。获得性大疱性表皮松解症的疾病谱包括一些病例，其疾病严重程度与之前仅在隐性营养不良型大疱性表皮松解症中才被认识到的严重程度相近。
