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左无名动脉的分离：何时进行手术？

Isolation of the left innominate artery: When to operate?

作者信息

Parsons Samuel J H, Nuttall Harry, Jones Alexander

机构信息

Department of Paediatric Cardiology, Oxford University Hospital NHS Foundation Trust, Oxford, UK.

Department of Paediatric Cardiology, Royal Brompton and Harefield Hospitals, Guy's and St. Thomas' NHS Foundation Trust, London, UK.

出版信息

Ann Pediatr Cardiol. 2024 Jan-Feb;17(1):74-76. doi: 10.4103/apc.apc_191_23. Epub 2024 May 24.

DOI:10.4103/apc.apc_191_23
PMID:38933045
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11198939/
Abstract

A right aortic arch with an isolated left innominate artery from the pulmonary artery is an exceedingly rare congenital cardiac malformation. We describe the management and complex surgical timing considerations in two such cases, successfully operated on day 4 and 7 months of age, including the use of cranial ultrasound as a helpful tool to guide decision-making. We also describe the first reported association of this defect with a 4q25 deletion encompassing the gene.

摘要

右位主动脉弓伴发自肺动脉的孤立性左无名动脉是一种极其罕见的先天性心脏畸形。我们描述了两例此类病例的治疗及复杂的手术时机考量，这两例分别在4日龄和7月龄时成功接受手术，包括使用头颅超声作为指导决策的有用工具。我们还描述了该缺陷与包含 基因的4q25缺失的首次报道关联。

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1
Isolation of the left innominate artery: When to operate?左无名动脉的分离：何时进行手术？
Ann Pediatr Cardiol. 2024 Jan-Feb;17(1):74-76. doi: 10.4103/apc.apc_191_23. Epub 2024 May 24.
2
Right-sided aortic arch with isolation of the left innominate artery and hypoplasia of the left internal carotid artery.右位主动脉弓伴左无名动脉隔离和左颈内动脉发育不良。
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Incomplete isolation of the left innominate artery from the right aortic arch: a rare case of double-outlet right ventricle with pulmonary stenosis.左无名动脉与右主动脉弓未完全分离：一例罕见的合并肺动脉狭窄的右心室双出口病例。
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The formal pathogenesis of isolated common carotid or innominate arteries: the concept of malseptation of the aortic sac.孤立性颈总动脉或无名动脉的正式发病机制：主动脉囊分隔异常的概念。
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Surgical Palliation of Right Aortic Arch With an Isolated Innominate Artery From the Left Ductus Arteriosus.左动脉导管起源的孤立无名动脉伴右主动脉弓的外科姑息治疗
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Isolation of the left common carotid or left innominate artery.分离左颈总动脉或左无名动脉。
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Anomalous origin of right pulmonary artery from innominate artery: Repair using pulmonary artery pedicled flap plasty.右肺动脉起自无名动脉异常：采用肺动脉带蒂瓣成形术修复。
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本文引用的文献

1
Prenatal genetic analysis of fetal aberrant right subclavian artery with or without additional ultrasound anomalies in a third level referral center.三级转诊中心胎儿异常右锁骨下动脉的产前遗传学分析，伴或不伴其他超声异常。
Sci Rep. 2023 Feb 28;13(1):3414. doi: 10.1038/s41598-023-30598-9.
2
LEF1 haploinsufficiency causes ectodermal dysplasia.Lef1 杂合不足导致外胚层发育不良。
Clin Genet. 2020 Apr;97(4):595-600. doi: 10.1111/cge.13714. Epub 2020 Feb 17.
3
A case of right aortic arch with isolated left innominate artery and global cerebral white matter atrophy.
一例右位主动脉弓伴孤立性左无名动脉及全脑白质萎缩。
Cardiol Young. 2019 Aug;29(8):1107-1109. doi: 10.1017/S1047951119001537. Epub 2019 Jul 10.
4
Isolation of the left brachiocephalic artery revisited: A 52-year literature review and introduction of a novel anatomic-clinical-prognostic classification.左头臂动脉分离术再探讨：52年文献综述及一种新的解剖-临床-预后分类法介绍
Ann Pediatr Cardiol. 2019 May-Aug;12(2):117-129. doi: 10.4103/apc.APC_74_18.
5
Wnt/β-catenin signaling enables developmental transitions during valvulogenesis.Wnt/β-连环蛋白信号通路在瓣膜发生过程中促成发育转变。
Development. 2016 Mar 15;143(6):1041-54. doi: 10.1242/dev.130575. Epub 2016 Feb 18.
6
Isolation of the left innominate artery: a question of connection.左无名动脉的分离：连接问题
J Cardiovasc Med (Hagerstown). 2016 Dec;17 Suppl 2:e164-e165. doi: 10.2459/JCM.0000000000000363.
7
Isolated innominate artery from the main pulmonary artery in DiGeorge syndrome.DiGeorge综合征中源自主肺动脉的孤立无名动脉。
J Am Coll Cardiol. 2011 Feb 8;57(6):753. doi: 10.1016/j.jacc.2010.03.110.
8
Right aortic arch and isolated left innominate artery from a left sided patent ductus arteriosus: a very rare aortic arch anomaly.右位主动脉弓及源自左侧动脉导管未闭的孤立性左无名动脉：一种非常罕见的主动脉弓异常。
J Pediatr Surg. 2009 Apr;44(4):E29-31. doi: 10.1016/j.jpedsurg.2009.01.002.
9
Anomalies of the derivatives of the aortic arch system.主动脉弓系统衍生物的异常。
Med Clin North Am. 1948 Jul;32:925-49. doi: 10.1016/s0025-7125(16)35662-0.
10
Ventricular and atrial septal defects, and right aortic arch associated with isolation of the left innominate artery from the aorta.室间隔和房间隔缺损，以及右位主动脉弓伴左无名动脉与主动脉分离。
Heart. 2000 Jan;83(1):99-100. doi: 10.1136/heart.83.1.99.