Khot Rachita, Shelman Nathan R, Ludwig Daniel R, Nair Rashmi T, Anderson Mark A, Venkatesh Sudhakar K, Paspulati Raj Mohan, Parker Rex A, Menias Christine O
Radiology and Medical Imaging, University of Virginia, Charlottesville, VA, USA.
Department of Pathology, University of Kentucky, Lexington, KY, USA.
Abdom Radiol (NY). 2025 Jan;50(1):152-168. doi: 10.1007/s00261-024-04462-x. Epub 2024 Jul 2.
Hepatic ductopenia is a pathologic diagnosis characterized by a decrease in the number of intrahepatic bile ducts as a consequence of various underlying etiologies. Some etiologies, such as primary sclerosing cholangitis, primary biliary cholangitis, and ischemic cholangitis, often have distinctive imaging findings. In contrast, other causes such as chronic rejection following liver transplantation, drug-induced biliary injury, infection, malignancy such as lymphoma, and graft-versus-host disease may only have ancillary or non-specific imaging findings. Thus, diagnosing ductopenia in conditions with nonspecific imaging findings requires a multidimensional approach, including clinical evaluation, serological testing, imaging, and liver histology to identify the underlying cause. These etiologies lead to impaired bile flow, resulting in cholestasis, liver dysfunction, and, ultimately, cirrhosis and liver failure if the underlying cause remains untreated or undetected. In the majority of instances, individuals diagnosed with ductopenia exhibit a positive response to treatment addressing the root cause or cessation of the causative agent. This article focuses on acquired causes of ductopenia, its clinical manifestation, histopathology, imaging diagnosis, and management.
肝内胆管减少是一种病理诊断,其特征是由于各种潜在病因导致肝内胆管数量减少。一些病因,如原发性硬化性胆管炎、原发性胆汁性胆管炎和缺血性胆管炎,通常有独特的影像学表现。相比之下,其他病因,如肝移植后的慢性排斥反应、药物性胆汁损伤、感染、淋巴瘤等恶性肿瘤以及移植物抗宿主病,可能只有辅助性或非特异性的影像学表现。因此,在影像学表现不特异的情况下诊断胆管减少需要采用多维度方法,包括临床评估、血清学检测、影像学检查和肝脏组织学检查,以确定潜在病因。这些病因会导致胆汁流动受损,进而引起胆汁淤积、肝功能障碍,如果潜在病因未得到治疗或未被发现,最终会导致肝硬化和肝衰竭。在大多数情况下,被诊断为胆管减少的个体对针对根本病因的治疗或停用致病因素会表现出积极反应。本文重点关注获得性胆管减少的病因、临床表现、组织病理学、影像学诊断和治疗。