Meguro Kentaro, Koitabashi Toshimi, Fujita Teppei, Ako Junya
Department of Cardiovascular Medicine, Kitasato University, 1-15-1 Kitasato, Minami-ku, Sagamihara, Kanagawa 252-0374, Japan.
Eur Heart J Case Rep. 2024 Jun 18;8(7):ytae299. doi: 10.1093/ehjcr/ytae299. eCollection 2024 Jul.
Right ventricular volume overload is the key finding in a patient with previously undiagnosed atrial septal defect (ASD).
A 68-year-old female was referred to our hospital due to progressive pulmonary artery dilatation observed on her chest X-ray. Echocardiography revealed a secundum ASD with right ventricular dilatation. She had undergone aortic root replacement and aortic valve replacement for annuloaortic ectasia and aortic insufficiency 12 years prior to the diagnosis. She was also diagnosed with Marfan syndrome, which was supported by family histories. Computed tomography did not show a secundum ASD before the surgery. We finally closed the secundum ASD with catheter closure device.
Ascending aneurysm might mask the presence of secundum ASD. Monitoring the change in pulmonary artery dilatation overtime is useful for the diagnosing secundum ASD.
右心室容量负荷过重是既往未诊断出的房间隔缺损(ASD)患者的关键表现。
一名68岁女性因胸部X线检查发现肺动脉进行性扩张而转诊至我院。超声心动图显示继发孔型ASD伴右心室扩张。她在诊断前12年因主动脉根部扩张和主动脉瓣关闭不全接受了主动脉根部置换和主动脉瓣置换术。她还被诊断出患有马凡综合征,家族史支持这一诊断。术前计算机断层扫描未显示继发孔型ASD。我们最终使用导管封堵装置闭合了继发孔型ASD。
升主动脉瘤可能掩盖继发孔型ASD的存在。长期监测肺动脉扩张的变化对诊断继发孔型ASD很有用。