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一例严重的糖尿病性腰骶神经根丛神经病:排除性诊断

A Severe Case of Diabetic Lumbosacral Radiculoplexus Neuropathy: A Diagnosis of Exclusion.

作者信息

Dao Kevin T, Leepakshi Johar, Abraham Jesslin, Aranguri Cesar M, Clarke Matthew, Ly Britney T, Veedu Hari K, Sabetian Katayoun

机构信息

Internal Medicine, University of California Los Angeles-Kern Medical Center, Bakersfield, USA.

Internal Medicine, Western University of Health Sciences, Pomona, USA.

出版信息

Cureus. 2024 Jun 8;16(6):e61969. doi: 10.7759/cureus.61969. eCollection 2024 Jun.

DOI:10.7759/cureus.61969
PMID:38978950
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11230586/
Abstract

Diabetic lumbosacral radiculoplexus neuropathy (DLSRPN), also known as diabetic amyotrophy, is a rare disease of exclusion that is difficult to diagnose due to its non-specific clinical presentation of neuropathy, autonomic symptoms, and potential weight loss. Due to this, many differential diagnoses are raised before making a diagnosis of such an uncommon disease. However, once the diagnosis is made, the management of this disease can vary. Here, we would like to discuss the etiology, pathophysiology, diagnosis, and management of this disease, as well as present a rare case of diabetic lumbosacral radiculoplexus neuropathy in a 50-year-old male.

摘要

糖尿病性腰骶神经根丛神经病(DLSRPN),也称为糖尿病性肌萎缩,是一种罕见的排除性疾病,因其神经病变、自主神经症状和潜在体重减轻的非特异性临床表现而难以诊断。因此,在诊断这种罕见疾病之前会进行许多鉴别诊断。然而,一旦确诊,这种疾病的治疗方法可能会有所不同。在此,我们将讨论该疾病的病因、病理生理学、诊断和治疗,并介绍一例50岁男性糖尿病性腰骶神经根丛神经病的罕见病例。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8381/11230586/62e0840c233f/cureus-0016-00000061969-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8381/11230586/0dd84b468078/cureus-0016-00000061969-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8381/11230586/62e0840c233f/cureus-0016-00000061969-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8381/11230586/0dd84b468078/cureus-0016-00000061969-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8381/11230586/62e0840c233f/cureus-0016-00000061969-i02.jpg

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本文引用的文献

1
AL amyloidosis presenting with isolated lumbosacral radiculoplexus neuropathy.孤立性腰骶神经根神经病表现的淀粉样变。
Pract Neurol. 2023 Nov 23;23(6):516-518. doi: 10.1136/pn-2023-003788.
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Diabetic Lumbosacral Radiculoplexus Neuropathy (Diabetic Amyotrophy).糖尿病性腰骶神经根丛神经病(糖尿病性肌萎缩)
Neurol Clin. 2020 Aug;38(3):553-564. doi: 10.1016/j.ncl.2020.03.010.
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Neurology. 2019 Mar 12;92(11):e1188-e1194. doi: 10.1212/WNL.0000000000007020. Epub 2019 Feb 13.
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Immunotherapy for diabetic amyotrophy.糖尿病性肌萎缩的免疫治疗
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Isolated amyloidosis presenting with lumbosacral radiculoplexopathy: description of two cases and pathogenic review.以腰骶神经根丛病为表现的孤立性淀粉样变性:两例病例描述及发病机制综述
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Diabetic and nondiabetic lumbosacral radiculoplexus neuropathies: new insights into pathophysiology and treatment.糖尿病性和非糖尿病性腰骶神经根丛神经病:病理生理学与治疗的新见解
Muscle Nerve. 2002 Apr;25(4):477-91. doi: 10.1002/mus.10080.
9
Methylprednisolone may improve lumbosacral radiculoplexus neuropathy.甲基强的松龙可能改善腰骶神经根丛神经病。
Can J Neurol Sci. 2001 Aug;28(3):224-7. doi: 10.1017/s0317167100001360.
10
Microvasculitis and ischemia in diabetic lumbosacral radiculoplexus neuropathy.糖尿病性腰骶神经根丛神经病中的微血管炎和缺血
Neurology. 1999 Dec 10;53(9):2113-21. doi: 10.1212/wnl.53.9.2113.