Butler James, Soni Aayesha, Melvill Roger
Constantiaberg Mediclinic, Cape Town, South Africa.
Division of Neurology, Department of Medicine, University of Cape Town, Cape Town, South Africa.
Epilepsy Behav Rep. 2024 Jun 21;27:100689. doi: 10.1016/j.ebr.2024.100689. eCollection 2024.
It is unclear whether a dominant hemispherectomy/hemispherotomy in someone with Rasmussen's Encephalitis (RE) may produce a satisfactory outcome when performed over the age of 40 years. Important questions include whether RE may continue to evolve three decades after onset, and whether a hemispherectomy may adequately shift language function when performed in older ages. Two cases illustrate seizure, language, motor and functional outcomes after dominant hemispherotomies. The cases were selected from an epilepsy surgery database of procedures performed at a private hospital in Cape Town, South Africa, spanning the period 1998-2023. A man in his 40s with epilepsy since childhood and dominant hemisphere RE partially regained impaired comprehension and ambulation, while expressive language function did not recover post-hemispherotomy. By contrast, a young teenage patient with dominant hemisphere RE demonstrated considerable recovery of expressive and receptive language and ambulation post-surgery. Both remain seizure-free. These two cases demonstrate that a dominant hemispherotomy, when performed on a quadragenarian, may produce a satisfactory, albeit inferior, functional outcome in comparison to when performed in childhood. RE may cause progressive neurological dysfunction in the late thirties and older and should be considered in patients presenting with functional decline decades after disease onset.
对于患有拉斯穆森脑炎(RE)的患者,在40岁以上进行优势半球切除术/大脑半球切开术是否能产生令人满意的结果尚不清楚。重要的问题包括RE在发病三十年后是否可能继续发展,以及在老年时进行半球切除术是否能充分转移语言功能。两个病例说明了优势半球切开术后的癫痫发作、语言、运动和功能结果。这些病例选自南非开普敦一家私立医院1998年至2023年期间进行的癫痫手术数据库。一名40多岁自童年起就患有癫痫且患有优势半球RE的男性部分恢复了受损的理解能力和行走能力,而半球切开术后表达性语言功能未恢复。相比之下,一名患有优势半球RE的青少年患者术后表达性和接受性语言以及行走能力有相当大的恢复。两人均无癫痫发作。这两个病例表明,与儿童期进行优势半球切开术相比,在四十多岁的患者中进行该手术可能会产生令人满意的功能结果,尽管效果较差。RE可能在三十多岁及以上的患者中导致进行性神经功能障碍,对于发病数十年后出现功能衰退的患者应予以考虑。