Department of Otolaryngology and Cervicofacial Surgery, Hassan II University Hospital, Fes, Morocco.
Pan Afr Med J. 2024 Apr 5;47:168. doi: 10.11604/pamj.2024.47.168.43187. eCollection 2024.
Conductive hearing loss with a normal tympanic membrane is a common reason for otolaryngology consultation, with otospongiosis being the most frequent cause and House syndrome being extremely rare, requiring systematic investigation. We report the case of a 31-year-old woman who presented with conductive hearing loss with a normal tympanic membrane. A temporal bone computed tomography (CT) scan confirmed a House-Goodhill syndrome due to fixation of the malleus head. Surgical intervention was considered to remove the attic bone synostosis with the malleus head, resulting in a significant clinical improvement. The Goodhill syndrome is a rare condition that causes hearing loss with a normal eardrum. The surgery can highly improve the hearing function.
鼓膜正常的传导性听力损失是耳鼻喉科就诊的常见原因,耳硬化症是最常见的病因,而 House 综合征极为罕见,需要系统的检查。我们报告了一例 31 岁女性,她因鼓膜正常的传导性听力损失就诊。颞骨计算机断层扫描(CT)证实了镫骨固定导致的 House-Goodhill 综合征。考虑手术干预以去除带有镫骨头的鼓室天盖骨融合,从而显著改善了临床症状。Goodhill 综合征是一种导致鼓膜正常的听力损失的罕见病症。手术可以极大地改善听力功能。