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Guidelines on the Diagnosis and Treatment of Hypertrophic Cardiomyopathy - 2024.

作者信息

Fernandes Fabio, Simões Marcus V, Correia Edileide de Barros, Marcondes-Braga Fabiana Goulart, Coelho-Filho Otavio Rizzi, Mesquita Cláudio Tinoco, Mathias Junior Wilson, Antunes Murillo de Oliveira, Arteaga-Fernández Edmundo, Rochitte Carlos Eduardo, Ramires Felix José Alvarez, Alves Silvia Marinho Martins, Montera Marcelo Westerlund, Lopes Renato Delascio, Oliveira Junior Mucio Tavares de, Scolari Fernando Luis, Avila Walkiria Samuel, Canesin Manoel Fernandes, Bocchi Edimar Alcides, Bacal Fernando, Moura Lidia Zytynski, Saad Eduardo Benchimol, Scanavacca Mauricio Ibrahim, Valdigem Bruno Pereira, Cano Manuel Nicolas, Abizaid Alexandre Antonio Cunha, Ribeiro Henrique Barbosa, Lemos Neto Pedro Alves, Ribeiro Gustavo Calado de Aguiar, Jatene Fabio Biscegli, Dias Ricardo Ribeiro, Beck-da-Silva Luis, Rohde Luis Eduardo Paim, Bittencourt Marcelo Imbroinise, Pereira Alexandre da Costa, Krieger José Eduardo, Villacorta Junior Humberto, Martins Wolney de Andrade, Figueiredo Neto José Albuquerque de, Cardoso Juliano Novaes, Pastore Carlos Alberto, Jatene Ieda Biscegli, Tanaka Ana Cristina Sayuri, Hotta Viviane Tiemi, Romano Minna Moreira Dias, Albuquerque Denilson Campos de, Mourilhe-Rocha Ricardo, Hajjar Ludhmila Abrahão, Brito Junior Fabio Sandoli de, Caramelli Bruno, Calderaro Daniela, Farsky Pedro Silvio, Colafranceschi Alexandre Siciliano, Pinto Ibraim Masciarelli Francisco, Vieira Marcelo Luiz Campos, Danzmann Luiz Claudio, Barberato Silvio Henrique, Mady Charles, Martinelli Filho Martino, Torbey Ana Flavia Malheiros, Schwartzmann Pedro Vellosa, Macedo Ariane Vieira Scarlatelli, Ferreira Silvia Moreira Ayub, Schmidt Andre, Melo Marcelo Dantas Tavares de, Lima Filho Moysés Oliveira, Sposito Andrei C, Brito Flávio de Souza, Biolo Andreia, Madrini Junior Vagner, Rizk Stephanie Itala, Mesquita Evandro Tinoco

机构信息

Instituto do Coração (InCor) do Hospital das Clínicas da Faculdade de Medicina da Universidade de São Paulo (HCFMUSP), São Paulo, SP - Brasil.

Faculdade de Medicina de Ribeirão Preto da Universidade de São Paulo, Ribeirão Preto, SP - Brasil.

出版信息

Arq Bras Cardiol. 2024 Jul 26;121(7):e202400415. doi: 10.36660/abc.20240415.

DOI:10.36660/abc.20240415
PMID:39082572
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC12092053/
Abstract
摘要
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/fb6e87f41b87/0066-782X-abc-121-07-e202400415-en-gf20.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/2c461d67f7db/0066-782X-abc-121-07-e202400415-gf01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/9c6b106e18a9/0066-782X-abc-121-07-e202400415-gf02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/43a0ff02ed3b/0066-782X-abc-121-07-e202400415-gf03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/29317ed92051/0066-782X-abc-121-07-e202400415-gf04.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/628e423b6d77/0066-782X-abc-121-07-e202400415-gf05.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/68830c5ac324/0066-782X-abc-121-07-e202400415-gf06.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/845cd6f0dc57/0066-782X-abc-121-07-e202400415-gf07.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/70e8ebd390df/0066-782X-abc-121-07-e202400415-gf08.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/7e0bba10e312/0066-782X-abc-121-07-e202400415-gf09.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/18f22420e8a0/0066-782X-abc-121-07-e202400415-gf10.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/8d630dcb7f1c/0066-782X-abc-121-07-e202400415-gf11.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/69b8055f7a94/0066-782X-abc-121-07-e202400415-gf12.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/d2a06d35bade/0066-782X-abc-121-07-e202400415-gf13.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/92ba7c4dbc1d/0066-782X-abc-121-07-e202400415-gf14.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/5325682159c2/0066-782X-abc-121-07-e202400415-gf15.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/f522694ae98f/0066-782X-abc-121-07-e202400415-gf16.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/c981397521da/0066-782X-abc-121-07-e202400415-gf17.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/8715f5565890/0066-782X-abc-121-07-e202400415-gf18.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/b447cb5b91df/0066-782X-abc-121-07-e202400415-gf19.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/3c14c0a45b51/0066-782X-abc-121-07-e202400415-gf20.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/a9a37739776e/0066-782X-abc-121-07-e202400415-en-gf01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/fb2505fd2904/0066-782X-abc-121-07-e202400415-en-gf02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/9838372804dc/0066-782X-abc-121-07-e202400415-en-gf03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/88a7f7e23f29/0066-782X-abc-121-07-e202400415-en-gf04.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/2d14e5761e1f/0066-782X-abc-121-07-e202400415-en-gf05.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/fe18d0b0c14c/0066-782X-abc-121-07-e202400415-en-gf06.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/34cd13961ea3/0066-782X-abc-121-07-e202400415-en-gf07.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/bbdf118375b7/0066-782X-abc-121-07-e202400415-en-gf08.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/f0817bfa2126/0066-782X-abc-121-07-e202400415-en-gf09.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/11e322cadc41/0066-782X-abc-121-07-e202400415-en-gf10.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/674d6d110d0e/0066-782X-abc-121-07-e202400415-en-gf11.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/e9ac0da37c8a/0066-782X-abc-121-07-e202400415-en-gf12.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/d15d5118781b/0066-782X-abc-121-07-e202400415-en-gf13.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/b09da64eba01/0066-782X-abc-121-07-e202400415-en-gf14.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/5d3b7f7355cd/0066-782X-abc-121-07-e202400415-en-gf15.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/bab82e4158d6/0066-782X-abc-121-07-e202400415-en-gf16.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/2380815fe643/0066-782X-abc-121-07-e202400415-en-gf17.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/ae9e850597ee/0066-782X-abc-121-07-e202400415-en-gf18.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/2461065c0f7a/0066-782X-abc-121-07-e202400415-en-gf19.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/fb6e87f41b87/0066-782X-abc-121-07-e202400415-en-gf20.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/2c461d67f7db/0066-782X-abc-121-07-e202400415-gf01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/9c6b106e18a9/0066-782X-abc-121-07-e202400415-gf02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/43a0ff02ed3b/0066-782X-abc-121-07-e202400415-gf03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/29317ed92051/0066-782X-abc-121-07-e202400415-gf04.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/628e423b6d77/0066-782X-abc-121-07-e202400415-gf05.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/68830c5ac324/0066-782X-abc-121-07-e202400415-gf06.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/845cd6f0dc57/0066-782X-abc-121-07-e202400415-gf07.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/70e8ebd390df/0066-782X-abc-121-07-e202400415-gf08.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/7e0bba10e312/0066-782X-abc-121-07-e202400415-gf09.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/18f22420e8a0/0066-782X-abc-121-07-e202400415-gf10.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/8d630dcb7f1c/0066-782X-abc-121-07-e202400415-gf11.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/69b8055f7a94/0066-782X-abc-121-07-e202400415-gf12.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/d2a06d35bade/0066-782X-abc-121-07-e202400415-gf13.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/92ba7c4dbc1d/0066-782X-abc-121-07-e202400415-gf14.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/5325682159c2/0066-782X-abc-121-07-e202400415-gf15.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/f522694ae98f/0066-782X-abc-121-07-e202400415-gf16.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/c981397521da/0066-782X-abc-121-07-e202400415-gf17.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/8715f5565890/0066-782X-abc-121-07-e202400415-gf18.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/b447cb5b91df/0066-782X-abc-121-07-e202400415-gf19.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/3c14c0a45b51/0066-782X-abc-121-07-e202400415-gf20.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/a9a37739776e/0066-782X-abc-121-07-e202400415-en-gf01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/fb2505fd2904/0066-782X-abc-121-07-e202400415-en-gf02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/9838372804dc/0066-782X-abc-121-07-e202400415-en-gf03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/88a7f7e23f29/0066-782X-abc-121-07-e202400415-en-gf04.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/2d14e5761e1f/0066-782X-abc-121-07-e202400415-en-gf05.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/fe18d0b0c14c/0066-782X-abc-121-07-e202400415-en-gf06.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/34cd13961ea3/0066-782X-abc-121-07-e202400415-en-gf07.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/bbdf118375b7/0066-782X-abc-121-07-e202400415-en-gf08.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/f0817bfa2126/0066-782X-abc-121-07-e202400415-en-gf09.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/11e322cadc41/0066-782X-abc-121-07-e202400415-en-gf10.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/674d6d110d0e/0066-782X-abc-121-07-e202400415-en-gf11.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/e9ac0da37c8a/0066-782X-abc-121-07-e202400415-en-gf12.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/d15d5118781b/0066-782X-abc-121-07-e202400415-en-gf13.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/b09da64eba01/0066-782X-abc-121-07-e202400415-en-gf14.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/5d3b7f7355cd/0066-782X-abc-121-07-e202400415-en-gf15.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/bab82e4158d6/0066-782X-abc-121-07-e202400415-en-gf16.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/2380815fe643/0066-782X-abc-121-07-e202400415-en-gf17.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/ae9e850597ee/0066-782X-abc-121-07-e202400415-en-gf18.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/2461065c0f7a/0066-782X-abc-121-07-e202400415-en-gf19.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4868/12092053/fb6e87f41b87/0066-782X-abc-121-07-e202400415-en-gf20.jpg

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Arq Bras Cardiol. 2025 Jun 16;122(4):e20250185. doi: 10.36660/abc.20250185. eCollection 2025.
5
Septal Preparation for TAVR Using Radiofrequency Catheters in Patients With LVOT Obstruction: 1-Year Follow-Up.使用射频导管对左心室流出道梗阻患者进行经导管主动脉瓣置换术的间隔准备:1年随访
JACC Case Rep. 2025 Jun 11;30(14):103606. doi: 10.1016/j.jaccas.2025.103606.
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Prognostic Value of Nonsustained Ventricular Tachycardia in Hypertrophic Cardiomyopathy in a Brazilian Cohort: Comparison with World Literature.非持续性室性心动过速在巴西肥厚型心肌病队列中的预后价值:与世界文献的比较
Arq Bras Cardiol. 2025 Apr;122(5):e20240399. doi: 10.36660/abc.20240399.
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Clinical and Echocardiographic Particularities of Hypertrophic Cardiomyopathy in a Brazilian Population and its Prognostic Impact.巴西人群肥厚型心肌病的临床和超声心动图特征及其预后影响。
Arq Bras Cardiol. 2025 Apr;122(4):e20240640. doi: 10.36660/abc.20240640.
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The Complex Puzzle of Hypertrophic Phenotype: A Practical Approach for the Clinician.肥厚型表型的复杂谜题:临床医生的实用方法
Arq Bras Cardiol. 2025 Mar;122(1):e20240529. doi: 10.36660/abc.20240529.
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Validation of ACC/AHA and ESC Sudden Cardiac Death Risk Guidelines in Diverse Hypertrophic Cardiomyopathy Cohort: Stratification HCM Study.ACC/AHA和ESC心脏性猝死风险指南在不同肥厚型心肌病队列中的验证:分层肥厚型心肌病研究
Glob Heart. 2024 Dec 17;19(1):94. doi: 10.5334/gh.1380. eCollection 2024.
心肌桥合并肥厚型心肌病心血管后果的系统评价和荟萃分析。
Am J Cardiol. 2023 Feb 1;188:110-119. doi: 10.1016/j.amjcard.2022.10.059. Epub 2022 Dec 10.
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Posterior Wall Thickness Associates With Survival Following Septal Myectomy for Obstructive Hypertrophic Cardiomyopathy.室间隔心肌切除术治疗梗阻性肥厚型心肌病患者的术后存活与室间隔后壁厚度相关。
JACC Heart Fail. 2022 Nov;10(11):831-837. doi: 10.1016/j.jchf.2022.06.009. Epub 2022 Sep 7.
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Syncope in hypertrophic cardiomyopathy (part II): An expert consensus statement on the diagnosis and management.肥厚型心肌病中的晕厥(第二部分):关于诊断与管理的专家共识声明
Int J Cardiol. 2023 Jan 1;370:330-337. doi: 10.1016/j.ijcard.2022.10.153. Epub 2022 Oct 26.
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Brazilian Society of Cardiology Guidelines on the Analysis and Issuance of Electrocardiographic Reports - 2022.巴西心脏病学会心电图报告分析与发布指南 - 2022年
Arq Bras Cardiol. 2022 Oct;119(4):638-680. doi: 10.36660/abc.20220623.
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Differing strategies for sudden death prevention in hypertrophic cardiomyopathy.肥厚型心肌病猝死预防的不同策略。
Heart. 2023 Mar 27;109(8):589-594. doi: 10.1136/heartjnl-2020-316693.
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Genetic Basis of Childhood Cardiomyopathy.儿童心肌病的遗传学基础。
Circ Genom Precis Med. 2022 Dec;15(6):e003686. doi: 10.1161/CIRCGEN.121.003686. Epub 2022 Oct 11.
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Hypertrophic Cardiomyopathy and Pregnancy: A Retrospective Analysis From a Tertiary Care Hospital.肥厚型心肌病与妊娠:一家三级保健医院的回顾性分析。
Tex Heart Inst J. 2022 Sep 1;49(5). doi: 10.14503/THIJ-20-7427.
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Arrhythmia in hypertrophic cardiomyopathy: Risk prediction using contrast enhanced MRI, T1 mapping, and personalized virtual heart technology.肥厚型心肌病中的心律失常:应用对比增强 MRI、T1 映射和个性化虚拟心脏技术进行风险预测。
J Electrocardiol. 2022 Sep-Oct;74:122-127. doi: 10.1016/j.jelectrocard.2022.09.004. Epub 2022 Sep 17.