[未分化多形性心脏肉瘤完全切除后的致命结局：病例报告]
[Fatal outcome of complete resection of undifferentiated pleomorphic cardiac sarcoma : About a case].
作者信息
El Mourabit Yassin, Saadouni Youssef, Tribak Mohammed, Jaafar Rhissassi Mohamed, Sayah Rochdi, Laaroussi Mohamed
机构信息
Service de chirurgie cardiovasculaire A, Hôpital Ibn Sina, Université Med V, Rabat, Maroc.
Service de chirurgie cardiovasculaire A, Hôpital Ibn Sina, Université Med V, Rabat, Maroc.
出版信息
Ann Cardiol Angeiol (Paris). 2024 Dec;73(6):101769. doi: 10.1016/j.ancard.2024.101769. Epub 2024 Aug 8.
INTRODUCTION
Undifferentiated pleomorphic sarcoma (UPS) is a very rare malignant primary cardiac tumor with a poor prognosis.
OBSERVATION
A 34-year-old woman complained of dyspnea evolving in a febrile context with altered general condition: Transthoracic echocardiography (TTE) revealed a left intra-atrial mass measuring 51/26 mm in diameter. A thoracic computed tomography (CT) revealed a mass occupying the left atrium measuring 42/28/34 mm, associated with two pulmonary metastases. The cardiac mass was resected and the postoperative suites were fatal. Histological diagnosis was UPS.
CONCLUSION
We present an atypical case of invasive UPS, which was surgically resected and scheduled for radio-chemotherapy with a fatal outcome.
引言
未分化多形性肉瘤（UPS）是一种非常罕见的原发性心脏恶性肿瘤，预后较差。
观察
一名34岁女性主诉在发热情况下出现呼吸困难，全身状况改变：经胸超声心动图（TTE）显示左心房内有一个直径为51/26毫米的肿块。胸部计算机断层扫描（CT）显示一个占据左心房的肿块，大小为42/28/34毫米，伴有两个肺转移灶。心脏肿块被切除，但术后情况致命。组织学诊断为UPS。
结论
我们报告了一例侵袭性UPS的非典型病例，该病例接受了手术切除，并计划进行放化疗，但结果致命。
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