Arendt A, Bräuer A
Zentralbl Allg Pathol. 1985;130(5):437-9.
The life and scientific career of Hugo Kufs, a pioneer in the field of neuropathology, are traced. Sixty years ago he described the first adult case of amaurotic idiocy, Kufs' disease (adult neuronal ceroid lipofuscinosis), and recognized that the condition represented a disturbance in lipid metabolism.
神经病理学领域的先驱雨果·库夫斯的生平与科学事业得以追溯。六十年前，他描述了首例成人黑蒙性白痴病例，即库夫斯病（成人神经元蜡样脂褐质沉积症），并认识到这种病症代表着脂质代谢紊乱。
