Arab Hazem, Alsaffaf Yousef, Khallouf Saleem
Faculty of Medicine, Hama University, Hama, Syria.
General Surgery Department, Hama National Hospital, Hama, Syria.
SAGE Open Med Case Rep. 2024 Aug 16;12:2050313X241271815. doi: 10.1177/2050313X241271815. eCollection 2024.
Mesenteric cystic lymphangiomas are a rare benign abdominal malformation of lymphatic vessels, with an estimated incidence of 1 per 250,000. Clinical presentation ranges from asymptomatic masses to acute abdominal pain. Diagnostic investigation includes ultrasound, abdominal computed tomography, or magnetic resonance imaging. Complete surgical excision is the recommended treatment. We present an 11-year-old female with abdominal cramps, and a 6-month history of gradually developing distension, constipation, and polyuria, without the occurrence of vomiting. Clinical examination revealed a soft, movable, painless abdominal mass with dullness on palpation. Ultrasound showed multi-cavity cystic masses in the abdomen, and a contrast-enhanced computed tomography scan revealed a large multi-cavity cystic mass involving most of the abdomen. A complete surgical excision was performed, and microscopic examination confirmed the diagnosis of mesenteric cystic lymphangioma. This case underscores the importance of considering mesenteric cystic lymphangiomas in the differential diagnosis of abdominal masses in pediatric patients, even in rarer age groups. Imaging aids in diagnosis and surgery planning. Complete excision curbs the risk of infection and recurrences.
肠系膜囊性淋巴管瘤是一种罕见的腹部淋巴管良性畸形,估计发病率为每25万人中1例。临床表现从无症状肿块到急性腹痛不等。诊断性检查包括超声、腹部计算机断层扫描或磁共振成像。推荐的治疗方法是完整手术切除。我们报告一名11岁女性,有腹部绞痛症状,并有6个月逐渐加重的腹胀、便秘和多尿病史,未出现呕吐。临床检查发现腹部有一个柔软、可移动、无痛的肿块,触诊时有浊音。超声显示腹部有多腔囊性肿块,增强计算机断层扫描显示一个大的多腔囊性肿块累及大部分腹部。进行了完整的手术切除,显微镜检查确诊为肠系膜囊性淋巴管瘤。该病例强调了在儿科患者腹部肿块的鉴别诊断中考虑肠系膜囊性淋巴管瘤的重要性,即使在较罕见的年龄组中也是如此。影像学有助于诊断和手术规划。完整切除可降低感染和复发风险。