Department of Surgery, Cardiothoracic Surgery Unit, Usmanu Danfodiyo University Teaching Hospital, Sokoto, Nigeria.
Department of Surgery, Usmanu Danfodiyo University, Sokoto, Nigeria.
Afr J Paediatr Surg. 2024 Jul 1;21(3):198-200. doi: 10.4103/ajps.ajps_122_22. Epub 2023 Apr 10.
Coexisting congenital cystic adenomatous malformation of the lungs and severe pectus excavatum (PE) is an uncommon presentation that poses significant management challenges. Conventionally managed in a staged manner, there are increasing reports of superior outcomes with single-staged concurrent repair with minimally invasive techniques (video-assisted thoracoscopic surgery [VATS] and minimally invasive repair of PE [MIRPE]). The outcome of a single-stage open repair for both anomalies has not been previously reported to the best of our search. We report the successful single-stage management of a 9-month-old infant with both anomalies who had an open lobectomy and modified Ravitch procedure. We aim to report the feasibility and safety of a single-stage concurrent repair of both conditions using open techniques, as VATS and MIRPE are not readily available in our environment.
先天性肺囊性腺瘤样畸形合并重度漏斗胸(PE)较为少见,其治疗颇具挑战性。传统上采用分期治疗,目前越来越多的报道表明,采用微创技术(电视辅助胸腔镜手术[VATS]和微创漏斗胸矫正术[MIRPE])同期一次性治疗可获得更好的效果。据我们所知,此前尚无关于同期开放手术治疗这两种畸形的报道。我们报告了一例 9 月龄婴儿同时患有这两种疾病的成功治疗经验,该患儿接受了开放性肺叶切除术和改良 Ravitch 手术。我们旨在报告使用开放技术同期一次性治疗这两种疾病的可行性和安全性,因为 VATS 和 MIRPE 在我们的环境中不易获得。