Wiese J A, Gentry L R, Menezes A H
Department of Radiology, University of Iowa Hospitals and Clinics, Iowa City 52242.
Pediatr Neurol. 1985 Nov-Dec;1(6):361-6. doi: 10.1016/0887-8994(85)90073-6.
The bobble-head doll syndrome is a rare movement disorder; fewer than 40 cases have been reported. It is usually associated with cystic abnormalities in the region of the anterior third ventricle. Various physiologic mechanisms have been proposed but none of them has been substantiated. We report a patient with this syndrome produced by a suprasellar arachnoid cyst. The CSF dynamics were investigated with CT cisternography. The phenomenon was apparently the result of intermittent obstruction at the foramina of Monro, a feature which has not previously been reported in this condition. The head movement served to partially relieve intraventricular obstruction, by both a posterior displacement of the cyst away from the foramina of Monro and a reduction in cyst size. This finding supports the concept that the bobble-head syndrome may be a "learned" behavior which lessens the symptomatology of hydrocephalus related to foramina of Monro obstruction.
点头娃娃综合征是一种罕见的运动障碍；报告的病例少于40例。它通常与第三脑室前部区域的囊性异常有关。已经提出了各种生理机制，但均未得到证实。我们报告了一名由鞍上蛛网膜囊肿引起的该综合征患者。通过CT脑池造影研究了脑脊液动力学。这种现象显然是由于Monro孔间歇性梗阻所致，这一特征在此病症中此前尚未见报道。头部运动通过使囊肿向后移位远离Monro孔以及减小囊肿大小，起到了部分缓解脑室内梗阻的作用。这一发现支持了点头综合征可能是一种“习得性”行为的观点，这种行为可减轻与Monro孔梗阻相关的脑积水症状。
