Farah G R, Awidi A S
Eur J Surg Oncol. 1985 Mar;11(1):57-60.
A 22 year old male who bled profusely at operation for excision of an extensive scalp and facial neurofibromata is reported. He was found to have congenital hypofibrinogenaemia. It is suggested that hypofibrinogenaemia should be considered as a cause of excessive bleeding in cases of Von Recklinghausen's neurofibromatosis.
报告了一名22岁男性,在切除广泛的头皮和面部神经纤维瘤手术中大量出血。发现他患有先天性低纤维蛋白原血症。有人提出,在冯·雷克林豪森神经纤维瘤病病例中,低纤维蛋白原血症应被视为出血过多的一个原因。