特发性心室颤动——究竟有多“特发性”？
Idiopathic Ventricular Fibrillation - Just How Much Idiopathic is it?
作者信息
Lietava Samuel, Sepsi Milan, Novotny Tomas
机构信息
Department of Internal Medicine and Cardiology, University Hospital Brno and Faculty of Medicine, Masaryk University, 625 00 Brno, Czech Republic.
出版信息
Rev Cardiovasc Med. 2024 Aug 22;25(8):306. doi: 10.31083/j.rcm2508306. eCollection 2024 Aug.
Abstract
Idiopathic ventricular fibrillation is diagnosed in survivors of sudden cardiac death that has been caused by ventricular fibrillation without known structural or electrical abnormalities, even after extensive investigation. It is a common cause of sudden death in young adults. Although idiopathic ventricular fibrillation is a diagnosis of exclusion, in many cases only a partial investigation algorithm is performed. The aim of this review is to present a comprehensive diagnostic evaluation algorithm with a focus on diagnostic assessment of inherited arrhythmic syndromes and genetic background.
摘要
特发性心室颤动是在心脏性猝死幸存者中诊断出来的，这些猝死由心室颤动引起，且不存在已知的结构或电异常，即便经过广泛检查亦是如此。它是年轻成年人猝死的常见原因。虽然特发性心室颤动是一种排除性诊断，但在许多情况下，仅执行了部分检查算法。本综述的目的是提出一种全面的诊断评估算法，重点关注遗传性心律失常综合征的诊断评估和遗传背景。
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