Yasumura Hiroto, Tao Koji, Imada Ryo, Yamashita Yushi, Tateishi Naoki, Arata Kenichi, Kinjo Tamahiro
Department of Cardiovascular Surgery, National Hospital Organization Kagoshima Medical Center, Kagoshima, Japan.
Department of Cardiovascular Surgery, Kagoshima City Hospital, Kagoshima, Japan.
Radiol Case Rep. 2024 Aug 10;19(11):4766-4774. doi: 10.1016/j.radcr.2024.07.117. eCollection 2024 Nov.
A 63-year-old woman presented with a giant arteriovenous malformation (AVM) of the lower limbs associated with Parkes Weber syndrome (PWS). The AVM was supplied by 4 branches of the right profunda femoris artery and 4-stage embolization was performed. At 67 years of age, she developed a pseudoaneurysm due to the recanalization of a coiled profunda femoris artery branch arterial aneurysm. We performed re-embolization of the coiled profunda femoris artery and observed its shrinkage, but 2 months later, the pseudoaneurysm began to expand again, having a fatal course. This case indicates that battles against giant AVM-associated PWS follow a long and convoluted path. We present this case with reviewing 15 previously reported cases to improve our management of PWS.
一名63岁女性因下肢巨大动静脉畸形(AVM)合并帕克斯·韦伯综合征(PWS)前来就诊。该AVM由右侧股深动脉的4个分支供血,并进行了4期栓塞治疗。67岁时,她因股深动脉分支动脉动脉瘤的弹簧圈栓塞后再通形成假性动脉瘤。我们对股深动脉分支进行了再次栓塞,并观察到其缩小,但2个月后,假性动脉瘤再次开始扩大,最终导致致命结局。该病例表明,与巨大AVM相关的PWS的治疗过程漫长且复杂。我们通过回顾15例既往报道的病例来展示本病例,以改善我们对PWS的治疗。