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[Not Available].

作者信息

Peiris Michella Dinithi, Saaby Lotte, Byg Keld-Erik

机构信息

Reumatologisk Afdeling C, Odense Universitetshospital.

Hjertemedicinsk Afdeling B, Odense Universitetshospital.

出版信息

Ugeskr Laeger. 2024 Aug 19;186(34):V02240141. doi: 10.61409/V02240141.

DOI:10.61409/V02240141
PMID:39234884
Abstract

This case report describes a 40-year-old male patient with severe cardiac failure due to eosinophilic granulomatosis with polyangiitis (EGPA) and myocarditis. The fast diagnostic approach with cardiac MRI (CMR) and immunosuppressive treatment with glucocorticoid and cyclophosphamide near-normalized the patient's cardiac function. Myocarditis due to EGPA is rare, however life-threatening, so a systematic approach and early CMR should be considered in patients with known asthma presenting with eosinophilia and cardiac involvement.

摘要

本病例报告描述了一名40岁男性患者,因嗜酸性肉芽肿性多血管炎(EGPA)和心肌炎导致严重心力衰竭。通过心脏磁共振成像(CMR)的快速诊断方法以及使用糖皮质激素和环磷酰胺的免疫抑制治疗使患者的心功能接近正常。由EGPA引起的心肌炎很罕见,但危及生命,因此对于已知患有哮喘且出现嗜酸性粒细胞增多和心脏受累的患者,应考虑采用系统的方法并尽早进行CMR检查。

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