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Cardio-facio-cutaneous Syndrome with Severe Inflammatory Cutaneous Lesions: Dramatic Effect of Dupilumab.

作者信息

Altandi Sara A, Apoil Pol A, Mazereeuw-Hautier Juliette, Severino-Freire Maella

机构信息

Department of Dermatology, Reference Center for Rare Skin Diseases, Toulouse, France.

Institut Fédératif de Biologie (IFB) Paul Sabatier University, Toulouse, France.

出版信息

Acta Derm Venereol. 2024 Sep 5;104:adv40465. doi: 10.2340/actadv.v104.40465.

DOI:10.2340/actadv.v104.40465
PMID:39235050
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11388110/
Abstract
摘要
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7cff/11388110/d0a10f8049b3/ActaDV-104-40465-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7cff/11388110/9bf9c7c77de7/ActaDV-104-40465-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7cff/11388110/3ffa9b43f399/ActaDV-104-40465-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7cff/11388110/d0a10f8049b3/ActaDV-104-40465-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7cff/11388110/9bf9c7c77de7/ActaDV-104-40465-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7cff/11388110/3ffa9b43f399/ActaDV-104-40465-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7cff/11388110/d0a10f8049b3/ActaDV-104-40465-g003.jpg

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本文引用的文献

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Dupilumab Treatment Efficacy and Impact on Clinical Scores, Serum Biomarkers, and Itch in Adult Patients with Atopic Dermatitis: A Retrospective Analysis.度普利尤单抗治疗成人特应性皮炎的疗效及其对临床评分、血清生物标志物和瘙痒的影响：一项回顾性分析
J Asthma Allergy. 2023 Nov 9;16:1233-1240. doi: 10.2147/JAA.S433515. eCollection 2023.
2
IgE levels in patients with atopic dermatitis steadily decrease during treatment with dupilumab regardless of dose interval.无论剂量间隔如何，使用度普利尤单抗治疗期间，特应性皮炎患者的IgE水平会持续下降。
Clin Exp Allergy. 2023 Nov;53(11):1222-1225. doi: 10.1111/cea.14384. Epub 2023 Sep 12.
3
Dupilumab Improves Pruritus in Netherton Syndrome: A Case Study.
度普利尤单抗改善Netherton综合征的瘙痒：一项病例研究。
Children (Basel). 2022 Feb 24;9(3):310. doi: 10.3390/children9030310.
4
Successful treatment of Netherton syndrome with dupilumab: A case report and review of the literature.成功使用度普利尤单抗治疗 Netherton 综合征：病例报告及文献复习。
J Dermatol. 2022 Jan;49(1):165-167. doi: 10.1111/1346-8138.16253. Epub 2021 Dec 3.
5
Treatment options for DOCK8 deficiency-related severe dermatitis.DOCK8 缺陷相关严重皮炎的治疗选择。
J Dermatol. 2021 Sep;48(9):1386-1393. doi: 10.1111/1346-8138.15955. Epub 2021 May 27.
6
Hailey-Hailey disease treated with dupilumab: a case series.用度普利尤单抗治疗的黑利-黑利病：病例系列
Br J Dermatol. 2021 Sep;185(3):680-682. doi: 10.1111/bjd.20475. Epub 2021 Jul 5.
7
Treatment of Grover Disease With Dupilumab.使用度普利尤单抗治疗格罗弗病。
JAMA Dermatol. 2021 Mar 1;157(3):353-356. doi: 10.1001/jamadermatol.2020.5097.
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Refractory pruritus responds to dupilumab in a patient with TTC7A mutation.一名患有TTC7A突变的患者的难治性瘙痒对度普利尤单抗有反应。
JAAD Case Rep. 2020 Dec 10;8:9-12. doi: 10.1016/j.jdcr.2020.12.004. eCollection 2021 Feb.
9
Basics and recent advances in the pathophysiology of atopic dermatitis.特应性皮炎的病理生理学基础及最新进展。
J Dermatol. 2021 Feb;48(2):130-139. doi: 10.1111/1346-8138.15664. Epub 2020 Oct 29.
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Allergy. 2021 Jan;76(1):395-398. doi: 10.1111/all.14536. Epub 2020 Oct 8.