Sleiay Mouhammmed, Sleiay Bilal, Hussein Bassam, Jawad Ali, Hassan Bassam, Masri Mahmod, Stitieh Youmna, Alokla Abdulrahim, Mansour Marah
Faculty of medicine, Hama University, Hama.
Faculty of Medicine, Alandalus university, Tartus.
Ann Med Surg (Lond). 2024 Apr 4;86(9):5481-5485. doi: 10.1097/MS9.0000000000001991. eCollection 2024 Sep.
Cor triatriatum sinister (CTS) is an uncommon heterogeneous congenital cardiac defect that may manifest in adulthood when symptomatic blockage manifests due to a change in hemodynamic physiology or when a condition such as atrial fibrillation (AF) arises. The incidence of cor triatriatum with cardiomyopathy and congenital heart illness ranges from 0.1 to 0.4%.
The Department of Cardiology examined a 10-year-old girl for a diastolic murmur. The patient's medical history was ordinary, and no previously known co-morbid illnesses were present. Pneumonia was the patient's original medical condition. A cardiac murmur was also discovered during the physical examination, and the patient was forwarded for more research. Physical examination revealed just a diastolic murmur, which was noteworthy. The patient's care plan includes routine echocardiographic monitoring. Since the deformity was not clinically significant, surgical repair was not advised.
It is unclear what caused this flaw. A full, incomplete, or fenestrated septum may be the result of the common pulmonary vein failing to merge with the left atrium during embryonic development. The existence of a fibromuscular membrane, which separates the left atrium (LA) into two chambers-the proximal chamber receiving the pulmonary veins (PVs) and the distal chamber contains the mitral valves and LA appendages defines the disease.
The diagnostic procedure should be carried out in the optimal settings, however, in cases of frail health systems, employing accessible alternatives might help the early diagnosis. Early referral to a cardiologist is required in case of CTS suspicion.
左心三房心(CTS)是一种罕见的异质性先天性心脏缺陷,当由于血流动力学生理变化出现症状性梗阻或出现心房颤动(AF)等情况时,可能在成年期表现出来。合并心肌病和先天性心脏病的三房心发病率为0.1%至0.4%。
心脏病科对一名10岁女孩进行检查,以评估舒张期杂音。患者病史无异常,既往无已知合并疾病。患者最初的疾病是肺炎。体格检查时还发现了心脏杂音,遂将患者转诊进行进一步检查。体格检查仅发现舒张期杂音,这一点值得注意。患者的护理计划包括常规超声心动图监测。由于畸形在临床上不显著,不建议进行手术修复。
尚不清楚导致此缺陷的原因。常见肺静脉在胚胎发育过程中未能与左心房融合,可能导致完全、不完全或有窗孔的隔膜形成。存在纤维肌性隔膜将左心房(LA)分为两个腔室——近端腔室接收肺静脉(PVs),远端腔室包含二尖瓣和左心耳,这定义了该病。
诊断程序应在最佳条件下进行,然而,在卫生系统薄弱的情况下,采用可及的替代方法可能有助于早期诊断。怀疑患有CTS时,需要尽早转诊至心脏病专家处。