Institute for Stem Cell Research and Regenerative Medicine, Medical Faculty, Heinrich-Heine University Düsseldorf, 40225 Düsseldorf, Germany.
Zayed Centre for Research into Rare Diseases in Children (ZCR), EGA Institute for Women's Health, University College London (UCL), 20 Guilford Street, London WC1N 1DZ, UK.
Int J Mol Sci. 2024 Aug 28;25(17):9332. doi: 10.3390/ijms25179332.
Every individual at some point encounters the progressive biological process of aging, which is considered one of the major risk factors for common diseases. The main drivers of aging are oxidative stress, senescence, and reactive oxygen species (ROS). The renin-angiotensin-aldosterone system (RAAS) includes several systematic processes for the regulation of blood pressure, which is caused by an imbalance of electrolytes. During activation of the RAAS, binding of angiotensin II (ANG II) to angiotensin II type 1 receptor (AGTR1) activates intracellular nicotinamide adenine dinucleotide phosphate (NADPH) oxidase to generate superoxide anions and promote uncoupling of endothelial nitric oxide (NO) synthase, which in turn decreases NO availability and increases ROS production. Promoting oxidative stress and DNA damage mediated by ANG II is tightly regulated. Individuals with sodium deficiency-associated diseases such as Gitelman syndrome (GS) and Bartter syndrome (BS) show downregulation of inflammation-related processes and have reduced oxidative stress and ROS. Additionally, the histone deacetylase sirtuin-1 (SIRT1) has a significant impact on the aging process, with reduced activity with age. However, GS/BS patients generally sustain higher levels of sirtuin-1 (SIRT1) activity than age-matched healthy individuals. SIRT1 expression in GS/BS patients tends to be higher than in healthy age-matched individuals; therefore, it can be assumed that there will be a trend towards healthy aging in these patients. In this review, we highlight the importance of the hallmarks of aging, inflammation, and the RAAS system in GS/BS patients and how this might impact healthy aging. We further propose future research directions for studying the etiology of GS/BS at the molecular level using patient-derived renal stem cells and induced pluripotent stem cells.
每个人在某个时候都会经历渐进的生物衰老过程,衰老被认为是常见疾病的主要危险因素之一。衰老的主要驱动因素是氧化应激、衰老和活性氧(ROS)。肾素-血管紧张素-醛固酮系统(RAAS)包括几个系统过程,用于调节由电解质失衡引起的血压。在 RAAS 激活过程中,血管紧张素 II(ANG II)与血管紧张素 II 型 1 受体(AGTR1)结合,激活细胞内烟酰胺腺嘌呤二核苷酸磷酸(NADPH)氧化酶,产生超氧阴离子,并促进内皮型一氧化氮合酶(eNOS)解偶联,从而降低 NO 的可用性并增加 ROS 的产生。ANG II 介导的氧化应激和 DNA 损伤的促进受到严格调控。患有与钠缺乏相关疾病(如 Gitelman 综合征(GS)和 Bartter 综合征(BS))的个体表现出炎症相关过程的下调,并减少氧化应激和 ROS。此外,组蛋白去乙酰化酶 Sirtuin-1(SIRT1)对衰老过程有重大影响,随着年龄的增长其活性降低。然而,GS/BS 患者的 SIRT1 活性通常比年龄匹配的健康个体高。GS/BS 患者的 SIRT1 表达往往高于健康年龄匹配个体;因此,可以假设这些患者会朝着健康衰老的方向发展。在这篇综述中,我们强调了衰老、炎症和 RAAS 系统的标志性特征在 GS/BS 患者中的重要性,以及这如何影响健康衰老。我们进一步提出了未来的研究方向,即在分子水平上使用患者来源的肾干细胞和诱导多能干细胞研究 GS/BS 的病因。