Hasler K, Klink I
Dtsch Med Wochenschr. 1985 Oct 4;110(40):1531-4. doi: 10.1055/s-2008-1069042.
Von Willebrand-Jürgens syndrome was diagnosed in 53 patients on the basis of bleeding symptoms and blood clotting analytical findings. It was possible to classify the patients into four types using the recommendations of the European Thrombosis Research Organization. Type I, 56%, was most common, 15% belonged to type II, 13% to type III and 16% to type IV. Whereas type I corresponds to the so-called classical von Willebrand-Jürgens syndrome, types II-IV demonstrate the heterogeneity of the disease.
根据出血症状和凝血分析结果,53例患者被诊断为血管性血友病(Von Willebrand-Jürgens syndrome)。根据欧洲血栓形成研究组织的建议,可将患者分为四种类型。I型最为常见,占56%,15%属于II型,13%属于III型,16%属于IV型。I型对应所谓的经典血管性血友病,而II-IV型则显示出该疾病的异质性。