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埃勒斯-当洛综合征与膀胱憩室

Ehlers-Danlos syndrome and diverticula of the bladder.

作者信息

Breivik N, Refsum S, Oppedal B R, Vesterhus P

出版信息

Z Kinderchir. 1985 Aug;40(4):243-6. doi: 10.1055/s-2008-1059784.

Abstract

Cases of two boys, 6 and 4 years old respectively, with Ehlers-Danlos syndrome (EDS) and large bladder diverticula, are reported. Diverticulectomies were performed, but large diverticula reappeared in both patients. A connection between the increased extensibility of the connective tissue in EDS and the development of bladder diverticula is suggested.

摘要

报告了两名分别为6岁和4岁的男孩患有埃勒斯-当洛综合征(EDS)并伴有巨大膀胱憩室的病例。进行了憩室切除术,但两名患者的巨大憩室均再次出现。提示EDS中结缔组织伸展性增加与膀胱憩室的发生之间存在联系。

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