Merga Tafese Gudissa, Gebreselassie Hana Abebe, Ahmed Mohamed, Mohammed Mensur, Girma Hiwote
Pediatric Surgery Unit, Department of Surgery, St. Paul's Hospital Millennium Medical College, Addis Ababa, Ethiopia.
Pediatric Surgery Unit, Department of Surgery, St. Paul's Hospital Millennium Medical College, Addis Ababa, Ethiopia.
Int J Surg Case Rep. 2024 Nov;124:110362. doi: 10.1016/j.ijscr.2024.110362. Epub 2024 Sep 27.
Urethral duplication is a rare congenital urinary tract anomaly. Its association with male epispadias is extremely rare. Due to various anatomical types, patients with urethral duplication can have a wide range of clinical presentations. Managing epispadias associated with urethral duplication involves different techniques and one should identify the functional urethra before proceeding with the surgery. It is associated with better functional outcomes than bladder epispadias exstrophy.
We report a case of a 4-year-old male child presented with a complaint of urinary incontinence. After evaluation, he was diagnosed with Urethral duplication associated with penopubic epispadias. Epispadias repair with urethral advancement was done and the child had a smooth postoperative course.
Both urethral duplication and epispadias are rare congenital urinary tract anomalies. Urethral duplication associated with epispadias is extremely rare. Patient clinical presentation varies from incontinence to incidental findings. The diagnosis of urethral duplication in epispadias patients is usually missed preoperatively and even intraoperatively. The type of procedure going to be done depends on the type of urethral duplication. Management of these patients is associated with good functional outcomes.
Even though urethral duplication associated with epispadias is a rare congenital malformation, it should be carefully searched in male epispadias.
尿道重复是一种罕见的先天性尿路畸形。其与男性尿道上裂的关联极为罕见。由于存在多种解剖类型,尿道重复患者可能有广泛的临床表现。处理与尿道重复相关的尿道上裂涉及不同技术,在进行手术前应确定功能性尿道。与膀胱外翻尿道上裂相比,其功能预后更好。
我们报告一例4岁男性患儿,主诉为尿失禁。经评估,他被诊断为与耻骨前尿道上裂相关的尿道重复。实施了尿道前移尿道上裂修复术,患儿术后恢复顺利。
尿道重复和尿道上裂均为罕见的先天性尿路畸形。与尿道上裂相关的尿道重复极为罕见。患者的临床表现从尿失禁到偶然发现不等。尿道上裂患者中尿道重复的诊断通常在术前甚至术中都会被漏诊。将要进行的手术类型取决于尿道重复的类型。这些患者的治疗与良好的功能预后相关。
尽管与尿道上裂相关的尿道重复是一种罕见的先天性畸形,但在男性尿道上裂患者中应仔细排查。