Said Sameh M, Mashadi Ali, Essa Yasin, Erb Markus
Division of Pediatric and Adult Congenital Cardiac Surgery, Maria Fareri Children's Hospital and Westchester Medical Center, New York Medical College, Valhalla, New York, USA.
Division of Pediatric Cardiology, Boston Children's Health Physicians, Maria Fareri Children's Hospital, Valhalla, New York, USA.
JACC Case Rep. 2024 Sep 4;29(17):102495. doi: 10.1016/j.jaccas.2024.102495.
A 38-year-old man with a functional single ventricle secondary to hypoplastic left heart syndrome presented with exertional fatigue. His last palliation was an intra-atrial conduit Fontan procedure. Comprehensive evaluation showed elevated liver enzyme values and a small, calcified conduit. Successful conversion to a nonfenestrated extracardiac conduit Fontan was performed with normalization of his liver enzyme values.
一名38岁男性,因左心发育不全综合征继发功能性单心室,出现劳力性疲劳。他最近一次姑息手术是心房内管道Fontan手术。全面评估显示肝酶值升高,且有一个小的钙化管道。成功转换为非开窗心外管道Fontan手术,其肝酶值恢复正常。