Hellgren L Samuel, Stenman Adam, Jatta Kenbugul, Condello Vincenzo, Larsson Catharina, Zedenius Jan, Juhlin C Christofer
Department of Oncology-Pathology, Karolinska Institutet, Stockholm, Sweden.
Department of Pathology and Cancer Diagnostics, Karolinska University Hospital, Stockholm, Sweden.
Endocr Pathol. 2024 Dec;35(4):411-418. doi: 10.1007/s12022-024-09828-x. Epub 2024 Oct 4.
De-escalation of thyroid cancer treatment is crucial to prevent overtreatment of indolent disease, but it remains important to identify clinically aggressive cases. TERT promoter mutations are molecular events frequently associated with high-risk thyroid tumors with poor outcomes and may identify cases at risk of dissemination. In various international guidelines, small minimally invasive follicular thyroid carcinoma and oncocytic thyroid carcinoma (miFTC/miOTC) are classified as low-risk lesions and are not recommended adjuvant treatment. Our study aimed to explore the association between size-based risk assessment and TERT promoter mutations. Between 2019 and May 2024, 84 miFTCs/miOTCs diagnosed at our department underwent digital droplet PCR analysis targeting TERT promoter mutational hotspots C228T and C250T in clinical routine. TERT promoter mutations were found in 10 out of 84 cases (11.9%). Mutated cases were pT1 (n = 1), pT2 (n = 3), or pT3 (n = 6). Patients with mutated tumors were older compared to patients with wild-type tumors (median age of 71 years vs. 57 years, p = 0.041). There were no significant differences regarding patient sex, tumor size, Ki-67 labeling index, or the presence of distant metastases. Notably, 30% of mutations displayed variant allele frequencies < 10%, possibly suggesting subclonal events. To conclude, TERT promoter mutations in miFTCs and miOTCs were associated with higher patient age and were often suspected to be subclonal. However, they did not affect clinical outcomes, possibly due to short follow-up. Reflex testing for this genetic alteration in miFTCs and miOTCs could be justified regardless of tumor size, though the clinical benefit remains uncertain.
降低甲状腺癌的治疗强度对于防止惰性疾病的过度治疗至关重要,但识别临床侵袭性病例仍然很重要。端粒酶逆转录酶(TERT)启动子突变是与预后不良的高危甲状腺肿瘤经常相关的分子事件,可能识别出有播散风险的病例。在各种国际指南中,微小浸润性滤泡性甲状腺癌和嗜酸性细胞性甲状腺癌(miFTC/miOTC)被归类为低风险病变,不建议进行辅助治疗。我们的研究旨在探讨基于大小的风险评估与TERT启动子突变之间的关联。在2019年至2024年5月期间,我们科室诊断的84例miFTC/miOTC在临床常规中接受了针对TERT启动子突变热点C228T和C250T的数字液滴PCR分析。84例病例中有10例(11.9%)发现TERT启动子突变。突变病例为pT1(n = 1)、pT2(n = 3)或pT3(n = 6)。与野生型肿瘤患者相比,突变肿瘤患者年龄更大(中位年龄71岁对57岁,p = 0.041)。在患者性别、肿瘤大小、Ki-67标记指数或远处转移情况方面没有显著差异。值得注意的是,30%的突变显示变异等位基因频率<10%,可能提示亚克隆事件。总之,miFTC和miOTC中的TERT启动子突变与患者年龄较大相关,且常被怀疑是亚克隆性的。然而,它们并未影响临床结局,可能是由于随访时间短。对于miFTC和miOTC中的这种基因改变进行反射性检测可能是合理的,无论肿瘤大小如何,尽管临床益处仍不确定。