• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利:CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验

小核RNA测序揭示了三种扩张型心肌病突变类型中不同的功能性转录途径改变。

SnRNA-seq reveals differential functional transcriptional pathway alterations in three mutant types of dilated cardiomyopathy.

作者信息

Ding Rui, Cao Wenzhao, Chen Yongbo, Zhu Yanrui, Yin Dan

机构信息

State Key Laboratory of Biocatalysis and Enzyme Engineering, School of Life Science, Hubei University, Wuhan 430062, China.

State Key Laboratory of Biocatalysis and Enzyme Engineering, School of Life Science, Hubei University, Wuhan 430062, China.

出版信息

Int J Biol Macromol. 2024 Nov;281(Pt 3):136353. doi: 10.1016/j.ijbiomac.2024.136353. Epub 2024 Oct 11.

DOI:10.1016/j.ijbiomac.2024.136353
PMID:39395510
Abstract

Dilated cardiomyopathy (DCM) is a leading cause of heart failure, characterized by ventricular dilation, thinning of the ventricular walls, and systolic dysfunction in either the left or both ventricles, often accompanied by fibrosis. Human cardiac tissue is composed of various cell types, including cardiomyocytes (CMs), fibroblasts (FBs), endothelial cells (ECs), macrophages, lymphocytes and so on. In DCM patients, these cells frequently undergo functional and phenotypic changes, contributing to contractile dysfunction, inflammation, fibrosis, and cell death, thereby increasing the risk of heart failure. This study focuses on DCM patients with mutations (LMNA, RBM20, and TTN) and analyzes functional changes in subpopulations of four cardiac cell types. The study involves functional annotation of subpopulations within each cell type and explores the association between gene mutations and specific functions and pathways. Additionally, the SCENIC method is employed of a particular cell subpopulation with significant functional importance, aiming to identify key transcriptional regulators in specific cell states. By analyzing the expression levels of ligand-receptor pairs in vCM4, vFB2, EC5.0, T cells, and NK cells across the DCM mutant genotypes, we predicted their signaling pathways and communications. This research provides insights into the molecular mechanisms of DCM and potential therapeutic targets.

摘要

扩张型心肌病(DCM)是心力衰竭的主要原因,其特征为心室扩张、心室壁变薄以及左心室或双心室收缩功能障碍,常伴有纤维化。人体心脏组织由多种细胞类型组成,包括心肌细胞(CMs)、成纤维细胞(FBs)、内皮细胞(ECs)、巨噬细胞、淋巴细胞等。在DCM患者中,这些细胞经常发生功能和表型变化,导致收缩功能障碍、炎症、纤维化和细胞死亡,从而增加心力衰竭的风险。本研究聚焦于具有(LMNA、RBM20和TTN)突变的DCM患者,并分析四种心脏细胞类型亚群的功能变化。该研究涉及对每种细胞类型内亚群的功能注释,并探索基因突变与特定功能和途径之间的关联。此外,对具有重要功能的特定细胞亚群采用SCENIC方法,旨在识别特定细胞状态下的关键转录调节因子。通过分析DCM突变基因型中vCM4、vFB2、EC5.0、T细胞和NK细胞中配体-受体对的表达水平,我们预测了它们的信号通路和通讯。本研究为DCM的分子机制和潜在治疗靶点提供了见解。

相似文献

1
SnRNA-seq reveals differential functional transcriptional pathway alterations in three mutant types of dilated cardiomyopathy.小核RNA测序揭示了三种扩张型心肌病突变类型中不同的功能性转录途径改变。
Int J Biol Macromol. 2024 Nov;281(Pt 3):136353. doi: 10.1016/j.ijbiomac.2024.136353. Epub 2024 Oct 11.
2
A mutation in the glutamate-rich region of RNA-binding motif protein 20 causes dilated cardiomyopathy through missplicing of titin and impaired Frank-Starling mechanism.RNA 结合蛋白 20 的谷氨酸丰富区的突变通过肌联蛋白的错剪接和弗兰克-斯塔尔机制受损导致扩张型心肌病。
Cardiovasc Res. 2016 Oct;112(1):452-63. doi: 10.1093/cvr/cvw192. Epub 2016 Aug 5.
3
Severe DCM phenotype of patient harboring RBM20 mutation S635A can be modeled by patient-specific induced pluripotent stem cell-derived cardiomyocytes.携带有 RBM20 突变 S635A 的患者表现出严重的扩张型心肌病表型,可以通过患者特异性诱导多能干细胞衍生的心肌细胞来模拟。
J Mol Cell Cardiol. 2017 Dec;113:9-21. doi: 10.1016/j.yjmcc.2017.09.008. Epub 2017 Sep 21.
4
Titin-truncating mutations associated with dilated cardiomyopathy alter length-dependent activation and its modulation via phosphorylation.与扩张型心肌病相关的肌联蛋白截断突变改变了其依赖长度的激活及其通过磷酸化的调节。
Cardiovasc Res. 2022 Jan 7;118(1):241-253. doi: 10.1093/cvr/cvaa316.
5
-Related Dilated Cardiomyopathy: Single-Cell Transcriptomics during Patient-Derived iPSC Differentiation Support Cell Type and Lineage-Specific Dysregulation of Gene Expression and Development for Cardiomyocytes and Epicardium-Derived Cells with Lamin A/C Haploinsufficiency.相关扩张型心肌病:患者来源 iPSC 分化过程中的单细胞转录组学研究支持肌细胞和心外膜衍生细胞的基因表达和发育的细胞类型和谱系特异性失调,伴有核纤层蛋白 A/C 单倍不足。
Cells. 2024 Sep 3;13(17):1479. doi: 10.3390/cells13171479.
6
A Novel Titin Truncation Variant Linked to Familial Dilated Cardiomyopathy Found in a Japanese Family and Its Functional Analysis in Genome-Edited Model Cells.一种与家族性扩张型心肌病相关的新型 Titin 截断变异在一个日本家庭中的发现及其在基因组编辑模型细胞中的功能分析。
Int Heart J. 2021 Mar 30;62(2):359-366. doi: 10.1536/ihj.20-664. Epub 2021 Mar 6.
7
Single-cell insights: pioneering an integrated atlas of chromatin accessibility and transcriptomic landscapes in diabetic cardiomyopathy.单细胞洞察:开创糖尿病性心肌病染色质可及性和转录组景观综合图谱。
Cardiovasc Diabetol. 2024 Apr 25;23(1):139. doi: 10.1186/s12933-024-02233-y.
8
DNA Damage Response/TP53 Pathway Is Activated and Contributes to the Pathogenesis of Dilated Cardiomyopathy Associated With LMNA (Lamin A/C) Mutations.DNA 损伤反应/TP53 通路被激活并有助于伴有 LMNA(核纤层蛋白 A/C)突变的扩张型心肌病的发病机制。
Circ Res. 2019 Mar 15;124(6):856-873. doi: 10.1161/CIRCRESAHA.118.314238.
9
The Combined Human Genotype of Truncating and Mutations Is Associated with Severe and Early Onset of Dilated Cardiomyopathy.截断和突变的联合人类基因型与扩张型心肌病的严重和早发有关。
Genes (Basel). 2021 Jun 8;12(6):883. doi: 10.3390/genes12060883.
10
RBM20 Mutations Induce an Arrhythmogenic Dilated Cardiomyopathy Related to Disturbed Calcium Handling.RBM20 突变导致心律失常性扩张型心肌病与钙处理紊乱相关。
Circulation. 2018 Sep 25;138(13):1330-1342. doi: 10.1161/CIRCULATIONAHA.117.031947.